اهمیت شناخت سندرم Ehlers Danlos بوسیله دندانپزشکان: گزارش یک مورد

نویسندگان

  • جمالی, فریدون
  • کاظم زاده, افسر
چکیده مقاله:

This syndrome is a genetical disorder with symptoms result from deficit in the formation of connective tissue, especially collagen fiber biosynthesis. In these patients, there is hyperelasticity and fragility of the skin and mucosa. Injuries sever bleeding, internal bleeding and hemartrosis may be seen in these patients. Wounds leave scars after healing. There is recurrent dislocation of the joints, especially knee and temporomandibular joints. Dentists should know the symptoms of this syndrome and its complications during dental treatments.

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[Ehlers-Danlos syndrome].

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[Ehlers-Danlos syndrome].

The Ehlers-Danlos syndrome (EDS) comprises a heterogenous group of nine hereditary connective tissue disorders, characterized by hyperelasticity of skin and hypermobility of joints to differing extents. The skin is easily injured and wound healing is delayed. The majority of EDS patients belong to EDS-types I-III. The pathogenesis in these cases is not known, although recent data suggest a role...

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Ehlers-Danlos Syndrome Type VIII

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Ehlers-Danlos syndrome (type VIII).

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عنوان ژورنال

دوره 7  شماره None

صفحات  64- 69

تاریخ انتشار 1994-06

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