Introduction: Fabry disease (FD) is a rare in which cardiovascular events are one of its manifestations. Aortic and mitral valve involvement among manifestations, but due to the concern suture failure without enzyme replacement therapy (ERT), desire for surgery has been very low, reported cases have few. After introduction ERT, such patients gradually from different places, high cost it not pra...

STUDY OBJECTIVES The aim of this study was to evaluate the early and long-term outcomes in patients undergoing aortic root replacement (ARR) with the Bentall procedure. DESIGN Retrospective study. SETTING Cardiothoracic surgery unit. PATIENTS AND METHODS Between January 1986 and January 2002, 72 patients (mean age 58.3 +/- 12.4 years, 81.9% males) underwent ARR by means of a Bentall opera...

Methods Study group consisted of 90 consecutive patients who were operated using elective Bentall procedure for the aneurysm of the ascending aorta and aortic valve disease from 1997 to 2003 in a single tertiary care center. Patients were followed for eight years for mortality, LV ejection fraction and volume indices, as well as functional capacity as assessed by NYHA class. Echocardiographic m...

Acute aortic dissection (AAD) during pregnancy can be fatal to both the pregnant mother and the baby, particularly in patients with the Marfan syndrome. We report a case of the modified Bentall procedure in surgery for AAD in a 31-year-old pregnant woman at 24 weeks of gestation with the Marfan syndrome. The patient recovered well after the operation, but unfortunately, the fetus could not be s...

A 64-year old male who underwent a mechanical valve Bentall procedure at another institution presented 1 year postoperatively with fever and dyspnoea. Laboratory investigations revealed Candida albicans infection with a periprosthetic collection. Confusion as to whether the collection was infective endocarditis, a periprosthetic transudate or a mass of haemostatic plugs used intraoperatively wa...

We report an unusual case of an aortic type A dissection with a corpus alienum which compresses the right ventricle. The patient successfully underwent an aortic root replacement in deep hypothermia with re-implantation of the coronary arteries using a modified Bentall procedure and the resection of the corpus alienum. Intraoperative finding reveals 3 greatly adhered gauze compresses, which wer...