نتایج جستجو برای: cdkl5

تعداد نتایج: 205  

Journal: :Indian pediatrics 2015
Mahesh Kamate Mayank Detroja

Journal: :Molecular syndromology 2011
N Van der Aa M Van den Bergh N Ponomarenko L Verstraete B Ceulemans K Storm

We screened a cohort of 5 male and 20 female patients with a Rett spectrum disorder for mutations in the coding region of FOXG1, previously shown to cause the congenital variant of Rett syndrome. Two de novo mutations were identified. The first was a novel missense mutation, p.Ala193Thr (c.577G>A), in a male patient with congenital Rett syndrome, and the second was the p.Glu154GlyfsX301 (c.460d...

Journal: :Arquivos De Neuro-psiquiatria 2023

Case presentation: S.S.A, 2 years old, female, born at term, with no complications during pregnancy, intrapartum, or neonatal period, and history of neurological diseases in the family. At months 20 days age, she presented her first convulsive crises, initially 3 8 crises successive days, duration seconds, which patient expressed muscular rigidity upper lower limbs. Due to progressive increase ...

Journal: :Pediatric neurology 2012
Mario Mastrangelo Vincenzo Leuzzi

Early-onset epileptic encephalopathies are severe disorders in which cognitive, sensory, and motor development is impaired by recurrent clinical seizures or prominent interictal epileptiform discharges during the neonatal or early infantile periods. They include Ohtahara syndrome, early myoclonic epileptic encephalopathy, West syndrome, Dravet syndrome, and other diseases, e.g., X-linked myoclo...

Journal: :Cell 2012
Michael E. Talkowski Jill A. Rosenfeld Ian Blumenthal Vamsee Pillalamarri Colby Chiang Adrian Heilbut Carl Ernst Carrie Hanscom Elizabeth Rossin Amelia M. Lindgren Shahrin Pereira Douglas Ruderfer Andrew Kirby Stephan Ripke David J. Harris Ji-Hyun Lee Kyungsoo Ha Hyung-Goo Kim Benjamin D. Solomon Andrea L. Gropman Diane Lucente Katherine Sims Toshiro K. Ohsumi Mark L. Borowsky Stephanie Loranger Bradley Quade Kasper Lage Judith Miles Bai-Lin Wu Yiping Shen Benjamin Neale Lisa G. Shaffer Mark J. Daly Cynthia C. Morton James F. Gusella

Balanced chromosomal abnormalities (BCAs) represent a relatively untapped reservoir of single-gene disruptions in neurodevelopmental disorders (NDDs). We sequenced BCAs in patients with autism or related NDDs, revealing disruption of 33 loci in four general categories: (1) genes previously associated with abnormal neurodevelopment (e.g., AUTS2, FOXP1, and CDKL5), (2) single-gene contributors to...

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