نتایج جستجو برای: congenital hyperinsulinism

تعداد نتایج: 124753  

2013
Gregory M. Martin Pei-Chun Chen Prasanna Devaraneni Show-Ling Shyng

ATP-sensitive potassium (KATP) channels link cell metabolism to membrane excitability and are involved in a wide range of physiological processes including hormone secretion, control of vascular tone, and protection of cardiac and neuronal cells against ischemic injuries. In pancreatic β-cells, KATP channels play a key role in glucose-stimulated insulin secretion, and gain or loss of channel fu...

Journal: :Hormone research 2006
Irina Giurgea Christine Bellanné-Chantelot Maria Ribeiro Laurence Hubert Christine Sempoux Jean-Jacques Robert Oliver Blankenstein Kahlid Hussain Francis Brunelle Claire Nihoul-Fékété Jacques Rahier Francis Jaubert Pascale de Lonlay

Congenital hyperinsulinism (CHI), characterized by profound hypoglycaemia related to inappropriate insulin secretion, may be associated histologically with either diffuse insulin hypersecretion or focal adenomatous hyperplasia, which share a similar clinical presentation, but result from different molecular mechanisms. Whereas diffuse CHI is of autosomal recessive, or less frequently of autosom...

2011
Courtney M. MacMullen Qing Zhou Kara E. Snider Paul H. Tewson Susan A. Becker Ali Rahim Aziz Arupa Ganguly Show-Ling Shyng Charles A. Stanley

OBJECTIVE Congenital hyperinsulinemic hypoglycemia is a group of genetic disorders of insulin secretion most commonly associated with inactivating mutations of the β-cell ATP-sensitive K(+) channel (K(ATP) channel) genes ABCC8 (SUR1) and KCNJ11 (Kir6.2). Recessive mutations of these genes cause hyperinsulinism that is unresponsive to treatment with diazoxide, a channel agonist. Dominant K(ATP) ...

Journal: :Medical Herald of the South of Russia 2020

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید