Acquired non-traumatic transethmoidal encephaloceles are very infrequent lesions that are generally caused by a tumor or hydrocephalus. As far as we know, there is no reported case of encephalocele after CSF diversion in the literature. We present a 25-year-old woman with hydrocephalus due to aquiductal stenosis who was treated with endoscopic third ventriculostomy. Nine months later, she had d...

In the present case we report about an encephalomeningocele in an adult female. Since the cause of this medical entity is a congenital fusion defect of the neural tube of the cranial base, most of the encephaloceles occurs in children leading to facial disfigurement. In the rare cases described in adults, rhinorrhea is usually present. Here we present a case of temporobasal encephalomeningocele...

Spontaneous encephaloceles are defined as brain herniations with no apparent cause. The aim of this paper is to describe the surgical technique performed in our department. We reviewed the last 3 cases treated with combined approach (transmastoid plus minicraniotomy) with 2-layer closure. In all cases the bone defects were located and successfully sealed. We had no postoperative complications. ...

Encephalocele is a mesodermal defect in the skull bones and duramater. Parietal encephalocele is a rare congenital anomaly of newborn with variable prognostic value. The authors report a case of a very large inter parietal encephalocele with no associated other system malformations. A midline inter parietal encephalocele is much rare, earlier reported cases were posterior parietal in location. ...

Anterior encephalocele (AE) is a rare congenital malformation in the central nervous system with a reportedly high prevalence in Assam, Northeast India. As there exists substantial variations in the etiology of the disease, determination of risk factors and timely intervention could reduce associated morbidity. A retrospective chart review of patients with AE who were born at or referred to Ass...

Erythropoietic Protoporphyria-Donaldson et al. BRmsH 663 eruptions. None of these show the characteristic clinical or biochemical findings. The infant in its pram may cry excessively during sunny weather. We have seen children and adults-not in this family-who were branded psychoneurotic because of emotional response to the burning sensation with absent or minimal skin changes. The mere assuran...

Objectives: To describe the versatility of acellular fetal bovine dermal matrix as an alternative to human cadaveric allograft for head and neck reconstructive procedures in children. Study Design: Case series with chart review. Methods: A database of pediatric operative procedures was queried for the use of acellular fetal bovine dermal matrix over a 16-month period. Indications for reconstruc...

Copyright © 2009 by the Congress of Neurological Surgeons Extended endoscopic endonasal approaches are becoming increasingly applied in the management of various intracranial pathol ogies along the midline cranial base. On one end of the complexity spectrum lie lesions such as pituitary adenomas and encephaloceles of the cribriform plate, which can be more easily approached through the endonasa...

Objectives/Hypothesis: The aim of this study is to indicate anatomic and immunologic peculiarities of the temporal bone which leave it vulnerable to traumatic, infectious and neoplastic insult. Study Design: Seven patients’ cases are described in which the clinical pathology of the temporal bone was bilateral. The bilaterality of these cases serves to illustrate the anatomic points which are th...