نتایج جستجو برای: ergic

تعداد نتایج: 979  

Journal: :Journal of cell science 2012
Duvinh Tran Antonious Chalhoub Allana Schooley Wendy Zhang Johnny K Ngsee

A proline to serine mutation (P56S) in vesicle-associated membrane protein-associated protein B and C (VAPB) causes an autosomal dominant form of amyotrophic lateral sclerosis (ALS). We show that the mutation also causes a nuclear envelope defect. Transport of nucleoporins (Nups) and emerin (EMD) to the nuclear envelope is blocked, resulting in their sequestration in dilated cytoplasmic membran...

Journal: :Science 2021

A brain circuit that drives and gates curiosity Curiosity is what organisms to investigate each other their environment. It considered by many be as intrinsic hunger thirst, but the neurobiological mechanisms behind have remained elusive. In mice, Ahmadlou et al. found a specific population of genetically identified ?-aminobutyric acid (GABA)—ergic neurons in region called zona incerta receive ...

Journal: :Indian journal of experimental biology 2002
Mohammad Ovais Sunita Rani Chimania

Effects of GABA-ergic agonists and antagonists were examined on the melanophores of a carp C. mrigala in vitro. GABA and baclofen both induced concentration - related dispersion in fish melanophores. Denervation of the melanophores by reserpine treatment potentiated the sensitivity of the melanophores to GABA. While denervation by cooling treatment inhibited the sensitivity of the melanophores ...

Journal: :Human mutation 2017
Leslie Matalonga Miren Bravo Carla Serra-Peinado Elisabeth García-Pelegrí Olatz Ugarteburu Silvia Vidal Maria Llambrich Ester Quintana Pedro Fuster-Jorge Maria Nieves Gonzalez-Bravo Sergi Beltran Joaquin Dopazo Francisco Garcia-Garcia François Foulquier Gert Matthijs Philippa Mills Antonia Ribes Gustavo Egea Paz Briones Frederic Tort Marisa Girós

Congenital disorders of glycosylation (CDG) are a heterogeneous and rapidly growing group of diseases caused by abnormal glycosylation of proteins and/or lipids. Mutations in genes involved in the homeostasis of the endoplasmic reticulum (ER), the Golgi apparatus (GA), and the vesicular trafficking from the ER to the ER-Golgi intermediate compartment (ERGIC) have been found to be associated wit...

2012
Dianshuai Gao Yi Liu Shen Sun Li Li Ye Xiong

Parkinson's disease (PD) is a degenerative disease of the central nervous system (CNS) predominantly occurring in older adults, and is particularly common after the age of 60. The primary pathologic characteristics of PD are neuronal degeneration and cell death of dopaminergic (DA-ergic) neurons, leading to a decrease in the dopamine (DA) level in the striatum. Originally extracted and purified...

2018
Ishier Raote Maria Ortega-Bellido António Jm Santos Ombretta Foresti Chong Zhang Maria F Garcia-Parajo Felix Campelo Vivek Malhotra

Collagen export from the endoplasmic reticulum (ER) requires TANGO1, COPII coats, and retrograde fusion of ERGIC membranes. How do these components come together to produce a transport carrier commensurate with the bulky cargo collagen? TANGO1 is known to form a ring that corrals COPII coats, and we show here how this ring or fence is assembled. Our data reveal that a TANGO1 ring is organized b...

2015
Makoto Ujike Fumihiro Taguchi

The envelopes of coronaviruses (CoVs) contain primarily three proteins; the two major glycoproteins spike (S) and membrane (M), and envelope (E), a non-glycosylated protein. Unlike other enveloped viruses, CoVs bud and assemble at the endoplasmic reticulum (ER)-Golgi intermediate compartment (ERGIC). For efficient virion assembly, these proteins must be targeted to the budding site and to inter...

Journal: :Cell 1998
William C Nichols Uri Seligsohn Ariella Zivelin Valeri H Terry Colette E Hertel Matthew A Wheatley Micheline J Moussalli Hans-Peter Hauri Nicola Ciavarella Randal J Kaufman David Ginsburg

Combined deficiency of factors V and VIII is an autosomal recessive bleeding disorder resulting from alterations in an unknown gene on chromosome 18q, distinct from the factor V and factor VIII genes. ERGIC-53, a component of the ER-Golgi intermediate compartment, was mapped to a YAC and BAC contig containing the critical region for the combined factors V and VIII deficiency gene. DNA sequence ...

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