نتایج جستجو برای: monogenic diseases

تعداد نتایج: 852089  

Journal: :Современные проблемы науки и образования (Modern Problems of Science and Education) 2015

2013
Hugo Varet Fabienne Jabot-Hanin Jean-Philippe Jais

Exome sequencing is becoming a standard tool for gene mapping of monogenic diseases. Given the vast amount of data generated by Next Generation Sequencing techniques, identification of disease causal variants is like finding a needle in a haystack. The impact assessment and the prioritization of potential pathogenic variants are expected to reduce work in biological validation, which is long an...

2013
S Fingerhutova A Kolsky D Rowczenio H Lachmann Z Vernerova F Votava P Dolezalova

Introduction AA amyloidosis may develop as a consequence of chronic inflammatory conditions including autoinflammatory diseases(AID). Mevalonate-kinase(MVK) deficiency(MKD) appears to be the least frequent underlying condition among monogenic periodic syndromes. Moreover, amyloidosis rarely manifests during childhood. We report a case of a small child in whom renal biopsy performed because of t...

Journal: :Muscles 2023

Limb-girdle muscular dystrophies (LGMDs) represent a group of muscle diseases due to monogenic mutations encoding proteins that are defective for heterozygous and homozygous prevalent in certain regions. Advances knowledge their pathophysiology have shed light on these rare diseases, which were, until recently, difficult diagnose. This paper has described the process diagnosis autosomal recessi...

2013
Jacques P Tremblay Xiao Xiao Annemieke Aartsma-Rus Carlos Barbas Helen M Blau Adam J Bogdanove Kym Boycott Serge Braun Xandra O Breakefield Juan A Bueren Michael Buschmann Barry J Byrne Michele Calos Toni Cathomen Jeffrey Chamberlain Marinee Chuah Kenneth Cornetta Kay E Davies J George Dickson Philippe Duchateau Terence R Flotte Daniel Gaudet Charles A Gersbach Renald Gilbert Joseph Glorioso Roland W Herzog Katherine A High Wenlin Huang Johnny Huard J Keith Joung Depei Liu Dexi Liu Hanns Lochmüller Lawrence Lustig Jeffrey Martens Bernard Massie Fulvio Mavilio Jerry R Mendell Amit Nathwani Katherine Ponder Matthew Porteus Jack Puymirat Jude Samulski Shin'ichi Takeda Adrian Thrasher Thierry VandenDriessche Yuquan Wei James M Wilson Steve D Wilton John H Wolfe Guangping Gao

The Harvard community has made this article openly available. Please share how this access benefits you. Your story matters. Boycott, et al. 2013. Translating the genomics revolution: the need for an international gene therapy consortium for monogenic diseases. Molecular Therapy 21(2): 266-268.

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید