Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA), also known as Herlyn-Werner-Wunderlich syndrome, is a rare syndrome with only a few hundred reported cases described since 1922. Only a handful of these cases have been associated with pyocolpos. Mullerian duct anomalies have an incidence of 2-3%. While OHVIRA constitutes 0.16-10% of these Mullerian duct anomalies. Symptoms usually p...

We would like to make some comments about the article “Persistent mullerian duct syndrome: a rare entity with a rare presentation in need of multidisciplinary management” (1). The authors report a DSD case diagnosed as PMDS and review some clinical aspects of this exceedingly rare syndrome, but some unclear aspects are notable. The patient described seems to be a case of ambiguous genitalia (pr...

OBJECTIVE To assess the efficacy of arterial duct angioplasty in maintaining adequate ductal patency in neonates with critical pulmonary valve stenosis. PATIENTS Two neonates presenting with cyanosis due to critical pulmonary valve stenosis with severe right ventricular hypoplasia underwent percutaneous balloon dilatation of the pulmonary valve. Despite successful dilatation, both remained cy...

Introduction. Zinner syndrome is a rare congenital malformation characterized by ipsilateral renal agenesis or hypoplasia, seminal vesicle cysts, and ejaculatory duct obstruction. Patients are usually asymptomatic develop unspecific symptoms. Case Report. We present case of 22-year-old male patient who presented with painless terminal hematuria. The denied trauma other urinary tract Magnetic re...