نتایج جستجو برای: pfapa

تعداد نتایج: 261  

Journal: :Pediatria i Medycyna Rodzinna 2023

Recurrent fever syndromes are autoinflammatory diseases. In their pathogenesis, no autoantibodies or autoreactive T-lymphocytes found. Innate immunity and adaptive of great importance in this case. the mid-latitudes, most common syndrome is periodic with aphthous stomatitis, pharyngitis cervical adenitis (PFAPA), which mainly affects children under 5 years age. Fevers occur cyclically, on avera...

2013
F Salehzadeh M Vahedi S Jahangiri S Hosseiniasl

Introduction Marshall Syndrome or PFAPA is an inflammatory periodic disease characterized by periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis. Restless, headache, abdominal pain, vomiting, hepatosplenomegaly and arthralgia are less common symptoms seeing in this disease. The diagnosis is established on the basis of clinical criteria that require the presence of a recurrent...

2011
Silvia Federici G Calcagno Martina Finetti Romina Gallizzi Antonella Meini A Vitale F Caroli M Cattalini Roberta Caorsi Francesco Zulian Alberto Tomasini A Insalaco J Frenkel Mariapia Sormani M Baldi Isabella Ceccherini Alberto Martini Marco Gattorno

Methods 113 caucasian patients carrying MEFV mutations (46 with mutations in two alleles, 67 heterozygous) and 205 genetically negative patients for MEFV, TNFSF1A and MEFV (70% with a PFAPA phenotype) were analyzed. The following groups were considerd: patients with: i) 2 high penetrance mutations (M694V, M694I, M680I), ii) 1 high, 1 low penetrance mutation, iii) 2 low penetrance mutations, iv)...

2017
Erato Atsali Dimitra Kassara Pelagia Katsimbri Sorina Boiu Dimitrios T. Boumpas Vana Papaevangelou Olena A. Oshlyanska Ludmila I. Omelchenko Tatiana A. Ljudvik Katerina Bouchalova Marcel Schüller Jana Franova Jarmila Skotakova Marie Macku Antoni Fellas Fiona Hawke Derek Santos Andrea Coda Anthi Kelempisioti Paula Keskitalo Virpi Glumoff Petri Kulmala Paula Vahasalo Mohammed A. Mozaffar Asraa K. Turkistani Samaa O. Sangoof Vladislav Sevostyanov Elena Zholobova Evangelia Bountouvi konstantinos Theodoropoulos Renata Moutsiou Christina Tsalapaki Talia Diaz Sofia Osorio Maria Teresa Braña Yuridiana Ramirez Luis Aparicio Andres Rodriguez Enrique Faugier Rocio Maldonado Maria Francesca Gicchino Carmela Granato Giulia Macchini Daniela Capalbo Alma Nunzia Olivieri Nathan Hasson Achille Marino Sona Narula Melissa Lerman Maria Amelia Muñoz Calonge Sara Maria Murias Loza Rosa Maria Alcobendas Agustin Remesal Esmeralda Núñez-Cuadros Rocio Galindo Zavala Gisela Díaz-Cordovés Rego Cristina Antúnez Fernández Yaiza García Molina Antonio L. Urda Cardona Nihal Sahin Habibe S. Durmus Ayse S. Pinarbasi Zubeyde Gunduz Muammer H. Poyrazoglu Zehra F. Karaman Turhan Oktem Mithat Oner Ruhan Dusunsel Gordana Susic Tamara Krstajic Dragana Vujovic Nedeljko Radlovic Zoran Lekovic Dusica Novakovic Gordana Milosevski Lomic Karina Mördrup Gunilla Hesselstrand Iva Sorić Lovro Lamot Mandica Vidovic Mirta Lamot Miroslav Harjacek Eva Adank Elvira Cannizzaro Schneider Eiman Abdalla Irfan Ullah L. Jeyaseelan Reem Abdwani Laila A. L. Shaqsi Ibrahim A. l. Zakwani Antonis Fanouriakis Mahesh Janarthanan Dhanarathnamoorthy Vetrichelvan P. Ramachandran Sangeetha Geminiganesan Dinesh Kumar Subba Rao Eleni-Maria Papatesta Despoina Maritsi Irini Eleftheriou Maria Tsolia Olga Vougiouka Mustafa Çakan Nuray Aktay Ayaz Şerife Gül Karadağ Gonca Keskindemirci Vladimir Keltsev Lyudmila Grebenkina Kwang Nam Kim Jong Gyun Ahn Young Dae Kim Maria Cristina Maggio Rolando Cimaz Maria Concetta Failla Piera Dones Mirella Collura Giovanni Corsello Jung-Woo Rhim Ki-Hwan Kim Soo-Young Lee Seung-Beom Han Jin-Han Kang Jae-Hee Chung Soo-Jung Lee Dae-Chul Jeong Andrei Santimov Regina Rupp Igor Alekseev Natalya Plutova Ekaterina Moskvina Marina Kruchina Aleksandra Tarasenko Natalya Sokolova Ekaterina Saveleva Ilia Bogdanov Dmitrii Ivanov Tatiana Kandrina Olga Kopanevich Anastasiia Grafskaia Natalia Ignateva Daria Pulukchu Natalia Pavlova Olga Kalashnikova Tatiana Kornishina Margarita Dubko Vyacheslav Chasnyk Mikhail Kostik Shama Sowdagar Janani Sankar Venkateswari Ramesh Iulia E. Szabo Claudia Sirbe Cristina Pamfil Laura Damian Simona Rednic Maria Deac Cristina Pamfil Mihaela Sparchez Ileana Filipescu Mirela Parvu Dumitrita Balint Ancuta Nicoara Simona Rednic Laura Damian

B1 Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome (PFAPA) in a 17 years old girl – case report Erato Atsali, Dimitra Kassara, Pelagia Katsimbri, Sorina Boiu, Dimitrios T. Boumpas, Vana Papaevangelou Pediatric Rheumatology Unit,3RD Department of Pediatrics, National and Kapodestrian University of Athens, Medical School, Athens, Greece; Joint Rheumatology Program,4TH De...

2008
P Scerbanovska P Dolezalova

Results Over the years 2004 – 2007 17 boys and 15 girls were diagnosed with PFAPA out of 87 patients referred to the fever clinic (36.8%). Median age at onset was 24 months (4–56), interval between attacks 4 weeks (2–12) and fever duration 3.5 days (1.5–7). Fever was generally above 39°C, associated with pharyngitis in 23 cases (71.9%), cervical adenitis in 24 (75%) and aphthous stomatitis in 1...

Journal: :Pediatric Rheumatology 2008

Journal: :Archives of Disease in Childhood 2012

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