This is a case report of an extremely rare cause of superior vena cava syndrome with systemic-to-pulmonary venous shunts, illustrated using different imaging modalities with successful SVC and IVC dilatation and stenting.

From the Departments of Therapeutic Radiology (L.D.W.) and Surgery (F.C.D.), Yale University School of Medicine; and the Yale Comprehensive Cancer Center (L.D.W., F.C.D.) — both in New Haven, CT; and the Department of Radiation Oncology, Memorial Sloan-Kettering Cancer Center, and Weill Medical College of Cornell University, New York ( J.Y.). Address reprint requests to Dr. Wilson at the Depart...

Superior vena cava syndrome has historically been associated with malignancy. With the increasing use of indwelling central lines, catheters, and pacemakers in the past decade, there have been an increasing number of cases associated with thrombosis rather than by direct external compression. Patients presenting to the ED with an acute process of SVC syndrome need to be assessed in a timely fas...