perlipidaemic with a positive family history for coronary artery disease (father) and diabetes mellitus (mother) was investigated for chest pain. The clinical examination gave no clear pathological findings. The ECG was normal. Blood biochemistry confirmed the reported hyperlipidaemia. The transthoracic echocardiogram showed a small dilatation of the right cardiac cavities. There was no atrial ...

The natural history of total pulmonary venous connection (TAPVC) is unfavorable per se. We describe a modified technique of intra-atrial repair in infants with supra- and infracardiac TAPVC. Twenty patients were treated. The median age at repair was 16 (range 3-62) days. Echocardiography and multi-detector row computed tomography were used to confirm the diagnosis. Our policy was to perform sur...

Surgical repair of total anomalous pulmonary venous connection (TAPVC) can be complicated by the development of pulmonary venous stenosis later on. In addition, the vertical vein, if left unligated, can remain patent and lead to hemodynamically significant left to right shunting. We report an infant who required transcatheter correction of both these problems after surgical repair of TAPVC.

FRIEDLOWSKY, in 1868, was the first to report total anomalous pulmonary venous connection.' 2 This entity, with its, multiple varieties,3 is receiving increasing attention with the recent encouraging reports of suecessful surgical therapy.4 The infradiaphragmatic form was first described by Ghon in 1916,5 and a total of 37 cases has since been reported.5 24 Obstruction to the pulmonary venous d...

1. Fulton DR, Soriano B. Partial anomalous pulmonary venous connection. In: Triedman JK, Kim MS, editors. UpToDate. 2013. Available from: http://www.uptodate.com [accessed 10.10.13]. 2. Sahay S, Krasuski RA, Tonelli AR. Partial anomalous pulmonary venous connection and pulmonary arterial hypertension. Respirology. 2012;17:957–63. 3. Brody H. Drainage of the pulmonary veins into the right side o...

Introduction: To present a rare occurrence of coronary sinus atrial septal defect (ASD) associated with total anomalous pulmonary venous connection (TAPVC). Case Report: A 16-year-old girl was diagnosed with features of an atrial septal defect (ASD) by transthoracic echocardiography and the absence of PLSVC (persistent left superior vena cava) connection to coronary sinus was confirmed by salin...

We describe a rare case of cyanosis following the Fontan operation with right-to-left shunting at the venous level, that is, an azygos venous to pulmonary venous connection. Few cases with partial anomalous pulmonary venous connection to azygos vein have been reported; however, there have been no reports describing the connection from azygos vein to pulmonary vein, which results in desaturation...