You have accessJournal of UrologyKidney Cancer: Epidemiology & Evaluation/Staging/Surveillance II (PD52)1 Sep 2021PD52-08 ANALYSIS OF RISK FACTORS FOR SURVIVAL AND PROGNOSIS PATIENTS WITH VON HIPPEL-LINDAU SYNDROME: A LARGE RETROSPECTIVE STUDY Kaifang Ma, Kenan Zhang, Jingcheng Zhou, Lin Cai, and Kan Gong MaKaifang Ma More articles by this author , ZhangKenan Zhang ZhouJingcheng Zhou CaiLin Cai...

The neurofibromatoses are members of the group of neurocutaneous disorders which also include tuberous sclerosis, neurocutaneous melanosis, hypomelanosis of Ito, incontinentia pigmenti, Sturge-Weber syndrome and von Hippel-Lindau disease. Collectively, these conditions have also been referred to as "phakomatoses," a term is derived from the Greek phakos, meaning a lentil or birthmark. All but S...

Received April 2007 Accepted October 2007 INTRODUCTION Recent investigations of the underlying pathophysiology of renal cell carcinoma (RCC) has resulted in the identification of involved molecular pathways, including the inactivation of the von Hippel-Lindau gene in most sporadic cases of RCC.(1) They are characterized by one specific histological type. In contrast, kidney tumors in patients w...

Von Hippel Lindau is an inherited disease which leads to tumor growth, including hemangioblastomas in the central nervous system and retina. No pharmacological treatment has demonstrated efficacy. Propranolol is a beta-blocker widely used in some neurological and cardiac diseases, and its safety is known. We present a patient diagnosed with Von Hippel Lindau disease who was treated with propran...