نتایج جستجو برای: wilms

تعداد نتایج: 3145  

2014
Linda Li Jennifer Light Michael Marchick Robyn Hoelle

Wilms tumor is found in 1 in 10,000 children and most commonly presents in asymptomatic toddlers whose care givers notice a nontender abdominal mass in the right upper quadrant. This case of Wilms tumor presented as a critically ill eleven-year old with significant tachypnea, dyspnea, vague abdominal pain, intermittent emesis, new onset seizure, metabolic acidosis, and hypoxemia. This is the fi...

2005
Bruce Broecker

Renal tumors other than Wilms’ tumor are infrequent in childhood. Wilms’ tumors account for 6% to 7% of childhood cancer, whereas the remaining renal tumors account for less than l%.27 The most common nonWilms‘ tumors are clear cell sarcoma of the kidney, rhabdoid tumor of the kidney (both formerly considered unfavorable Wilms’ tumor variants but now considered separate tumors), renal cell carc...

Journal: :Journal of clinical pathology 2005
R Fukuzawa R W Heathcott I M Morison A E Reeve

BACKGROUND Loss of imprinting (LOI) of the H19/IGF2 domain is a common feature of Wilms tumour. The GTL2/DLK1 domain is also imprinted and is structurally similar to H19/IGF2. The question arises as to whether DLK1 also undergoes LOI in Wilms tumour, or whether the LOI mechanism is restricted to the H19/IGF2 domain. AIM To investigate the imprinting status of DLK1 in Wilms tumours with IGF2 L...

Journal: :Atlas of Genetics and Cytogenetics in Oncology and Haematology 2011

Journal: :DMW - Deutsche Medizinische Wochenschrift 1918

2009
Kylie M. Drake E. Cristy Ruteshouser Rachael Natrajan Phyllis Harbor Jenny Wegert Manfred Gessler Kathy Pritchard-Jones Paul Grundy Jeffrey Dome Vicki Huff Chris Jones Micheala A. Aldred

Purpose: Wilms' tumor is a childhood cancer of the kidney with an incidence of ∼1 in 10,000. Cooccurrence of Wilms' tumor with 2q37 deletion syndrome, an uncommon constitutional chromosome abnormality, has been reported previously in three children. Given these are independently rare clinical entities, we hypothesized that 2q37 harbors a tumor suppressor gene important in Wilms' tumor pathogene...

Journal: :Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 2004
Min Hu Geoff Y Zhang Susan Arbuckle Nicole Graf Albert Shun Martin Silink Deborah Lewis Stephen I Alexander

BACKGROUND Denys-Drash syndrome (DDS) is associated with mutations of the Wilms' tumour 1 (WT1) gene, and is characterized by pseudohermaphroditism, a progressive glomerulopathy, and the development of Wilms' tumour. More than 90% of patients with DDS who carry constitutional intragenic WT1 mutations are at high risk (90%) for the development of Wilms' tumour. WT1 is a signalling protein with 9...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2012
Aleksandra Bielen Gary Box Lara Perryman Lynn Bjerke Sergey Popov Yann Jamin Alexa Jury Melanie Valenti Alexis de Haven Brandon Vanessa Martins Vincent Romanet Sebastien Jeay Florence I Raynaud Francesco Hofmann Simon P Robinson Suzanne A Eccles Chris Jones

We have previously demonstrated an increased DNA copy number and expression of IGF1R to be associated with poor outcome in Wilms tumors. We have now tested whether inhibiting this receptor may be a useful therapeutic strategy by using a panel of Wilms tumor cell lines. Both genetic and pharmacological targeting resulted in inhibition of downstream signaling through PI3 and MAP kinases, G(1) cel...

2017
Wen Fu Zhen-Jian Zhuo Wei Jia Jinhong Zhu Shi-Bo Zhu Ze-Feng Lin Feng-Hua Wang Huimin Xia Jing He Guo-Chang Liu

Wilms' tumor is one of the most prevalent pediatric malignancies, ranking fourth in childhood cancer worldwide. TP53 is a critical tumor suppressor gene, which encodes a 53 kDa protein, p53. The p53 functions to protect against cancer by regulating cell cycle and apoptosis and maintaining DNA integrity. TP53 gene is highly polymorphic. Several TP53 gene polymorphisms have been considered to be ...

Journal: :Journal of clinical pathology 1982
H B Marsden W Lawler

The incidence of renal dysplasia in a series of Wilms' tumours is presented. The distribution of such lesions is discussed, together with their course of development and regression. The kidney is regarded as a particularly suitable organ for studying the relation between dysplasia and neoplasia. A schema is suggested for this association with regard to Wilms' tumour.

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