نتایج جستجو برای: ژن myh7

تعداد نتایج: 16107  

Journal: :Circulation. Cardiovascular genetics 2010
Sek Won Kong Yong Wu Hu Joshua W K Ho Sadakatsu Ikeda Sean Polster Ranjit John Jennifer L Hall Egbert Bisping Burkert Pieske Cristobal G dos Remedios William T Pu

BACKGROUND Alternative mRNA splicing is an important mechanism for regulation of gene expression. Altered mRNA splicing occurs in association with several types of cancer, and a small number of disease-associated changes in splicing have been reported in heart disease. However, genome-wide approaches have not been used to study splicing changes in heart disease. We hypothesized that mRNA splici...

2015
Jianjun Zuo Fan Wu Yihua Liu Juan Xiao Mei Xu Qinping Yu Minhao Xia Xiaojun He Shigeng Zou Huize Tan Dingyuan Feng

Porcine skeletal muscle fibres are classified based on their different physiological and biochemical properties. Muscle fibre phenotype is regulated by several independent signalling pathways, including the mitogen-activated protein kinase (MAPK), nuclear factor of activated T cells (NFAT), myocyte enhancer factor 2 (MEF2) and peroxisome proliferator-activated receptor (PPAR) signalling pathway...

Journal: :American journal of physiology. Heart and circulatory physiology 2005
Norman R Alpert Saidi A Mohiddin Dorothy Tripodi Jacqueline Jacobson-Hatzell Kelly Vaughn-Whitley Christine Brosseau David M Warshaw Lameh Fananapazir

Autosomal dominant familial hypertrophic cardiomyopathy (FHC) has variable penetrance and phenotype. Heterozygous mutations in MYH7 encoding beta-myosin heavy chain are the most common causes of FHC, and we proposed that "enhanced" mutant actin-myosin function is the causative molecular abnormality. We have studied individuals from families in which members have two, one, or no mutant MYH7 alle...

Journal: :PLoS ONE 2007
Birgit S. Budde Priska Binner Stephan Waldmüller Wolfgang Höhne Wulf Blankenfeldt Sabine Hassfeld Jürgen Brömsen Anastassia Dermintzoglou Marcus Wieczorek Erik May Elisabeth Kirst Carmen Selignow Kirsten Rackebrandt Melanie Müller Roger S. Goody Hans-Peter Vosberg Peter Nürnberg Thomas Scheffold

Noncompaction of the ventricular myocardium (NVM) is the morphological hallmark of a rare familial or sporadic unclassified heart disease of heterogeneous origin. NVM results presumably from a congenital developmental error and has been traced back to single point mutations in various genes. The objective of this study was to determine the underlying genetic defect in a large German family suff...

2015
Wenyuan Zhao Tieqiang Zhao Yuanjian Chen Fengbo Zhao Qingqing Gu Robert W. Williams Syamal K. Bhattacharya Lu Lu Yao Sun Nikolaos Frangogiannis

Familial hypertrophic cardiomyopathy (HCM) is attributed to mutations in genes that encode for the sarcomere proteins, especially Mybpc3 and Myh7. Genotype-phenotype correlation studies show significant variability in HCM phenotypes among affected individuals with identical causal mutations. Morphological changes and clinical expression of HCM are the result of interactions with modifier genes....

2014
Tiziana Angrisano Gabriele Giacomo Schiattarella Simona Keller Gianluigi Pironti Ermanno Florio Fabio Magliulo Roberta Bottino Raffaela Pero Francesca Lembo Enrico Vittorio Avvedimento Giovanni Esposito Bruno Trimarco Lorenzo Chiariotti Cinzia Perrino

Re-induction of fetal genes and/or re-expression of postnatal genes represent hallmarks of pathological cardiac remodeling, and are considered important in the progression of the normal heart towards heart failure (HF). Whether epigenetic modifications are involved in these processes is currently under investigation. Here we hypothesized that histone chromatin modifications may underlie changes...

Journal: :PloS one 2015
Ahmad Amanzada Lars Reinhardt Dorothea Fey Elisabeth M Zeisberg Sabine Mihm

Genetic polymorphisms in the region of the interferon-λ genes (IFNL) associate with clearance of hepatitis C virus (HCV) infection. One of these polymorphisms, IFNL4 rs368234815, determines loss or gain of function of the IFNL4 gene by frameshift variation. The very same and a second one, IFNL3 rs4803217, are supposed to impact the expression of IFNL3: while IFNL4 rs368234815 is suggested to mo...

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