Staged surgical repair and interventional cardiac catheterization have contributed to improved outcomes for children with congenital heart disease. As a result, there are increasing numbers of children and adolescents who must undergo multiple invasive cardiac procedures at various developmental stages. During these procedures, management of pain and anxiety using nonpharmacological methods is ...

A full term boy was admitted with respiratory distress in the fourth week of his life due to spontaneous chylothorax in his right hemithorax. Spontaneous chylothorax occurred previously in a first cousin of the neonate establishing that way the final diagnosis of familial idiopathic congenital pneumothorax. Failure of the conservative treatment consisting of chest tube drainage, discontinuation...

X-linked myotubular myopathy usually presents at birth with hypotonia and respiratory distress. Phenotypic presentation, however, can be extreme variable. We report on a newborn baby, who presented with the severe form of the disease. In the second week of life, he developed a clinically relevant chylothorax, needing drainage and treatment with octreotide acetate. Pleural effusions are frequent...

chondroectodermal dysplasia (ellis-van creveld syndrome) is a rare autosomal recessive congenital abnormality. this syndrome is characterized by a spectrum of clinical findings, among which chondrodystrophy, polydactyly, ectodermal dysplasia, and congenital cardiac anomalies are the most common. it is imperative to not overlook the cardiac complications in patients with this syndrome during den...

As previous studies have revealed, postoperative chylothorax is a rare complication of cardiothoracic surgery procedures, especially myocardial revascularization [1–4]. It occurs in less than 1% of thoracic procedures [5] and 0.6%–0.8% of cases of cardiovascular surgery [6]. We describe a case of chylothorax that occurred a few days after coronary artery bypass grafting and which was treated on...

today, congenital heart diseases may be treated without surgery through advances in interventional cardiology. however, complications such as infection and thrombus formation may develop due to foreign materials used during these procedures. surgical intervention may be required for the removal of the device utilized for the procedure. in this case report, we present the surgical treatment of a...

OBJECTIVE Prior investigations have suggested that the rapidly growing population of adults with congenital heart disease is at increased risk of perioperative morbidity and mortality, but information is limited on the nature of those perioperative factors that may relate to adverse outcomes. We sought to use a national claims database to describe the contribution of perioperative factors to ad...

Pediatric intervcntional cardiology was conceived in the 1960s by Dr. William Rashkind, emerged as a distinct suhspccialty during the 198Os, and has come of age in the 1990s. At C.S. Mott Children’s Hospital, the number of interventional pediatric cardiac catheterizations has grown rapidly during the past decade (Fig. 1). Therapeutic procedures currently comprise 35%-40% of all cardiac catheter...

introduction: along with advances occurring in cardiopulmonary bypass (cpb) including improved anesthesia intubation and early surgical interventions, it has become possible to correct life-threatening congenital heart anatomic abnormalities in patients. our study aimed to collect information from one of the most important centers of pediatric cardiac surgery in iran since there is limited info...