The giant congenital lobar emphysema is a rare malformation infant pathology. The authors report a similar case which is distinguished by its segmental location even rare with its compressive character in which segmentectomy was successful performed to lift emergency distress in a developing country.

Miller-Dieker syndrome (MDS) is a rare genetic syndrome associated with lissencephaly, developmental delay, and high mortality. We describe a patient who was diagnosed postnatally with both MDS and congenital lobar emphysema. We believe that this is the first reported case of the two conditions presenting in the same patient.

process was impaired by inflammation.3,9 These observations were confirmed by means of gas analysis by Lindskog and Van Allen.A Collateral respiration was also demonstrated in relation to experimental segmental emphysema produced by valvular bronchial obstruction. Lobar emphysema followed valvular obstruction of lobar bronchi, but no emphysema resulted from this type of obstruction in the prima...