Primary cutaneous adenoid cystic carcinoma (PCACC) is a rare variant of adenoid cystic carcinoma (ACC) which originates from the skin adnexa, most probably eccrine and apocrine glands. This tumor has a head and neck predilection and also occurs in the chest, abdomen, back, and perineum. We hereby present a 63-year-old man with PCACC located on the shin. No previous similar case has been reporte...

background: giant retroperitoneal uterine leiomyomas are uncommon. degenerative changes of a leiomyoma may lead to unusual presentation resulting in misdiagnosis preoperatively. the final diagnosis can be made either intraoperatively or histologically. case: we report a 45-year-old multiparous women presented with abdominal distension and fatigue for six months. abdominopelvic sonography and co...

PURPOSE OF REVIEW Nutritional status in cystic fibrosis is important to the health and long-term survival of patients; however, children with cystic fibrosis are not achieving the dietary recommendations or achieving normal growth. This paper reviews current knowledge about behavioral and environmental barriers to dietary adherence in this population. RECENT FINDINGS Children with cystic fibr...

Cystic nephroma is a rare, benign multicystic lesion of the kidney. This tumor occurs both in children and in adults. In children, it is highly prevalent in males; in adults, it is more frequent in women. The term "cystic nephroma" represents two apparently different entities: pediatric cystic nephroma, a benign form thought to originate from metanephric tissue, and adult cystic nephroma, consi...

Biliary mucinous cystic neoplasms of the liver are rare cystic tumors comprising less than 5% of the liver cystic neoplasms. These tumors demonstrate a female predominance and entail a risk of malignant transformation. We present a 56-year-old female patient with a multiloculated liver cystic lesion measuring 22 cm who underwent a cystectomy with en bloc resection of the liver segments II, III,...

Cardiac cystic echinococcosis is a rarely encountered parasitic infestation caused by Echinococcus granulasus larvae. Cystic echinococcosis hydatid composes 0.5-2% of all human cystic echinococcosis cases. Isolated cardiac involvement is very rare. Cardiac cystic echinococcosis hydatid generally accompanies another organ involvement, however, it might be isolated as in the present case and alth...

Cystic sebaceous neoplasms have been seen only in patients with Muir-Torre syndrome (MTS) and have recently been characterized as marker lesions of MTS. Histologically, these lesions form a spectrum of tumors ranging from benign cystic adenomas to proliferative cystic sebaceous tumors. We describe 2 proliferative cystic sebaceous tumors in a 53-year-old man whose workup revealed colonic adenoca...

OBJECTIVES To assess left ventricular systolic and diastolic function in adult patients with cystic fibrosis using radionuclide ventriculography. BACKGROUND Although myocardial fibrosis has been described in autopsy specimens of patients with cystic fibrosis, the possibility that myocardial dysfunction may occur during life in adult patients with cystic fibrosis has not been explored. METHO...

Primary adenoid cystic carcinoma of the Bartholin gland is a rare carcinoma in female genitalia tract. In review of literature less than 100 cases have been reported. The presented case is a 44 - year - old married woman with complain of a painful mass in the vulvar area. The nodule was excised and microscopic examination revealed adenoid cystic carcinoma of Bartholin gland origin. A few months...

Lisa C. Grossman is a first-year medical student at Georgetown University,Washington, DC. in patients who have 10% or more CFTR function. Patients with 1% or less functioning of CFTR generally have a more classic type of cystic fibrosis; however, no definitive correlation exists between the genotype and the phenotype. In patients with 1% or less functioning of the gene, the patients’ cells have...