Desmoid tumors account for approximately 0.3% of all solid tumors. The chest wall represents 8-10% of all cases, and surgery is the primary treatment modality for sporadic resectable desmoid tumors. Currently, the term ‘‘sarcoma with low-grade malignancy’’ is preferred, due the tendency of these tumors toward local invasion and frequent recurrence, even after complete surgical resection. There ...

Desmoid tumor is a rare monoclonal fibroblast proliferation that is regarded as benign. The clinical management of desmoid tumors is very complex and requires a multidisciplinary approach because of the unpredictable disease course. For those cases localized in the anterior abdominal wall, symptomatic and unresponsive to medical treatment, radical resection and reconstruction with a prosthetic ...

The authors report the case of an adult female patient who developed a thoracic paraspinous desmoid tumor (aggressive fibromatosis) located just cranially to the incision scar of the previous surgery for resection of a spinal schwannoma. To the best of the authors' knowledge, this is the first report of an extraabdominal desmoid tumor occurring after resection of a spinal schwannoma. Desmoid tu...

Desmoid-type fibromatosis is a rare and locally aggressive monoclonal, fibroblastic proliferation characterized by a variable and often unpredictable clinical course. Currently, there is no established or evidence-based treatment approach available for this disease. Therefore, in 2015 the European Desmoid Working Group published a position paper giving recommendations on the treatment of this i...

INTRODUCTION Desmoid tumors are very rare, benign fibrous neoplasms arise from the musculoaponeurotic structures throughout the body. CASE REPORT The patient was a seven-year old boy with a large mandibular mass growing over a period of six months. His CT-scan showed a large mass, 13 cm in diameter in the cheek area extending to the neck and trachea. Biopsy was compatible with desmoid fibroma...

INTRODUCTION Desmoid tumor of bone is a rare benign tumor. It is reported commonly in mandibular and meta-diaphyseal region of long bones. We report involvement of unusual site in ilio-acetabular region with breach in articular cartilage. CASE REPORT A 40 year old female presented with pain in the left hip. Radiologically, a lytic lesion at ilio-acetabular region was seen. Intra-operatively b...

developed in association with silicone implants [4]. These lesions may develop after the implantation of either saline or silicone implants, but they develop more commonly when silicone implants are used. When a breast mass has developed after implant insertion, physicians must consider desmoid tumor and anaplastic large cell lymphoma in the diagnosis, although the incidence is low. This articl...

BACKGROUND Desmoid tumours or fibromatoses are rare entities characterized by the benign proliferation of fibroblasts, which can be life-threatening due to their locally aggressive properties. Surgery is widely accepted as the first line of treatment for extra-abdominal desmoids; however, it is not recommended for intra-abdominal desmoids because of the high-risk of recurrence and difficulties ...

Desmoid tumors, which are locally invasive with recurrence but without metastasis, are frequently observed in patients with familial adenomatous polyposis after abdominal surgery or during pregnancy. This study analyzed mutation of the adenomatous polyposis coli gene in 8 desmoid tumors from 7 familial adenomatous polyposis patients using polymerase chain reaction-single-strand conformation pol...

BACKGROUND Desmoid tumor represents a rare monoclonal neoplasm arising from deep musculoaponeurotic structures and may occur sporadically or in association with the familial adenomatous polyposis and Gardner syndromes. Desmoid tumors do not appear to demonstrate metastatic potential; however, local infiltrative growth results in significant morbidity and potential mortality. Although the deline...