Biotinidase deficiency is a disorder inherited autosomal recessively showing evidence of hearing loss and optic atrophy in addition to seizures, hypotonia, and ataxia. In the present study, a 2-year-old boy with Biotinidase deficiency is presented in which clinical symptoms have been reported with auditory neuropathy/auditory dyssynchrony (AN/AD). In this case, transient-evoked otoacoustic emis...

In 95 percent of the cases, patients with acoustic neuromas will have some magnitude of hearing loss in the affected ear. This paper reports on four patients who had acoustic neuromas and normal hearing. Results from the case history, audiometric evaluation, auditory brainstem response (ABR), electroneurography (ENOG), and vestibular evaluation are reported for each patient. For all patients, t...

The aim of the current study is to investigate hearing function in patients with allergic rhinitis. Fifty-eight patients with positive skin prick test (Group 1) (116 ears) and 31 subjects with negative skin prick test (62 ears) as group 2 were included. Pure tone audiometry at 250, 500, 1000, 2000, 4000 and 8000 Hz and immittance measures, including tympanometry and acoustic reflex tests, were ...

Abstract Background Hearing is commonly impaired in Behçet’s disease (BD). Also, vestibular abnormalities as well cochlear function affection have been found. The inflammatory process which leads to BD may be the cause of frequency audiometry those patients. aim this study assess hearing and vestibulo-colic reflex Behçet patients using convential pure-tone (cPTA), high-frequency (HFA), cervical...

This article provides an overview of four auditory disorders relevant generally to adults and especially to veterans. The disorders are noise-induced hearing loss, idiopathic sudden sensorineural hearing loss, otosclerosis, and Méniàre's disease. Sensorineural hearing loss characterizes each, but additional aspects vary with each of the four conditions. This article describes the conditions, di...

The current issue of the Iranian Rehabilitation Journal contains original research evaluating the efficacy of addiction rehabilitation an evaluation of a child rehabilitation system for community based research, reading program for children with down syndrome, auditory stream segregation in auditory processing disorder, speech and language disorders, quality of life of adolescents with hearing ...