نتایج جستجو برای: mefv gene mutations

تعداد نتایج: 1225908  

2015
Z Gunduz B Sozeri A Esen A Pac Kısaarslan H Kılıc R Dusunsel H Poyrazoglu M Dundar I Dursun

Objective Familial Mediterranean fever (FMF) is an autosomal recessive disease characterized by recurrent attacks of fever and peritonitis, pleuritis, arthritis or an erysipelaslike skin disorder. The disease may present at any age, more than 80% of patients being symptomatic by the age of 20 yr. Its main long-term complication is amyloid A (AA) amyloidosis, a severe manifestation with poor pro...

Journal: :The Israel Medical Association journal : IMAJ 2003
Nurit Zaks Yael Shinar Shai Padeh Merav Lidar Adam Mor Irena Tokov Mordechai Pras Pnina Langevitz Elon Pras Avi Livneh

BACKGROUND Familial Mediterranean fever is an autosomal recessive disease characterized by recurrent attacks of fever and serositis. The disease is caused by mutations in the MEFV gene, presumed to act as a down-regulator of inflammation within the polymorphonuclear cells. OBJECTIVES To present the results of 412 FMF patients genotyped for three MEFV mutations, M694V, V726A and E148Q. RESUL...

Journal: :Pediatric Rheumatology 2008

2014
Kiyoshi Migita Kazunaga Agematsu Masahide Yazaki Fumiaki Nonaka Akinori Nakamura Tomoko Toma Dai Kishida Ritei Uehara Yoshikazu Nakamura Yuka Jiuchi Junya Masumoto Hiroshi Furukawa Hiroaki Ida Chihiro Terai Yoshikazu Nakashima Atsushi Kawakami Tadashi Nakamura Katsumi Eguchi Michio Yasunami Akihiro Yachie

Familial Mediterranean fever (FMF) is an autoinflammatory disease caused by MEditerranean FeVer gene (MEFV) mutations. In Japan, patients with FMF have been previously reported, including a mild or incomplete form. Several factors are presumed to contribute to the variable penetrance and to the phenotypic variability of FMF. We conducted the current study to investigate the correlation of varia...

Journal: :Dicle Medical Journal / Dicle Tıp Dergisi 2009

Journal: :medical laboratory journal 0
farzane salarneia golestan university of medical sciences, gorgan, iran sare zhand golestan university of medical sciences, gorgan, iran behnaz khodabakhshi golestan university of medical sciences, gorgan, iran alijan tabarraei golestan university of medical sciences, gorgan, iran mohammad ali vakili golestan university of medical sciences, gorgan, iran naeme javid golestan university of medical sciences, gorgan, iran

abstract       background and objective: hepatitis b virus (hbv) is a dna virus with high tendency toward hepatic tissue. there are currently about 3 million hbv-infected people and 350 to 400 million chronic carriers of this virus in the world. x protein plays a role in the over-expression of oncogenes, carcinogenicity of liver cells and overlaps with the basal core promoter of the virus. muta...

Background: Familial Mediterranean fever (FMF) has episodic or subclinical inflammation that may lead to a decrease in bone mineral density (BMD). The objective of this study was to assess BMD in Egyptian children with FMF on genetic basis.Methods: A cross sectional study included 45 FMF patients and 25 control children of both sexes in the age range between 3-16 years old. The patients were re...

2013
F Gohar M Jeske P Lohse T Kallinich U Neudorf T Niehues H Wittkowski E Lainka D Foell

Introduction Familial Mediterranean fever (FMF) is one of the most common autoinflammatory diseases (AID). A variety of relevant mutations in the MEFV gene have been demonstrated. Pro-inflammatory S100 proteins correlate with disease activity in autoinflammatory disorders, and have been previously correlated with clinically active FMF. Here, we describe the association between these biomarkers ...

2015
G Sarrabay D Méchin B Dumont M André I Touitou

Introduction Familial mediterranean fever (FMF) is a rare monogenic disease and the prototype of autoinflammatory disorders. It is caused by mutations in the MEFV gene and is autosomal recessively inherited. Most mutations are missense substitutions, small deletions are quite rare, and only three nonsense mutation has been described (http://fmf.igh.cnrs. fr/ISSAID/infevers/). Large rearrangemen...

2015

© 2015 The Authors; Tabriz University of Medical Sciences This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/3.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. Prevalence of the MEFV gene mutations and their clinical correlati...

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