Mesenchymal chondrosarcoma is one of the most unusual, rare malignant cartilaginous tumors with unique histopathological appearance and biological behavior.1 Only around 50 cases affecting the jaws were reported in literature.2,3 It was first described by Lichtenstein and Bernstein in 1958 as a separate entity.1 It develops from pluripotent, mesenchymal stem cells and can differentiate into ang...

Mesenchymal chondrosarcoma is a rare skeletal tumor. Of the extraskeletal sites, the intracranial location is the most common, followed by the orbit and the soft tissues. First described by Lichtenstein and Bernstein in 1959, the histological feature is biphasic consisting of undifferentiated mesenchymal cells admixed with islands of cartilaginous tissue. Most intracranial tumors are meningeal-...

The current study presents a case of extraskeletal mesenchymal chondrosarcoma (ESMC) involving the vena cava that originally occurred in the retroperitoneum of a 61-year-old female. Following excision of the masses, pathological examination confirmed a diagnosis of primary ESMC. Mesenchymal chondrosarcomas are extremely rare in comparison to conventional chondrosarcomas and even more so when ar...

BACKGROUND We analyzed clinical and treatment-related factors influencing the outcome of patients with mesenchymal chondrosarcoma (MC). Twenty-six patients (median age, 31 years) were identified using the Tumor Center and Chemotherapy Department database of the study institute. METHODS Patients received surgery (24 patients) and/or radiotherapy (5 patients), and chemotherapy (12 patients). ...

Extraskeletal mesenchymal chondrosarcoma (EMCS) is a rare malignant cartilaginous tumor arising from the soft tissues. The most common areas of extraskeletal origin are the lower extremities, the orbits and the central nervous system, among others. In this study, the case of primary EMCS arising from the right buccal region in a 26-year old female is presented. Histological and immunohistochemi...

Extraskeletal mesenchymal chondrosarcoma (EMCS) is a rare malignant soft tissue tumor of chondroprogenitor cell origin. Originally, it was restricted to the bone only but that no longer case. Recent literature reports 20–33% these tumors occur at extraskeletal sites. We report one such case, in which involved anterior abdominal wall muscles and also had large intra- mass covered part peritoneal...