日本では神経耳科学的疾患（耳鳴，めまい，難聴等）に対して多くの漢方薬が使用されている。耳鳴，めまい患者の多くは耳科学的疾患以外の症候（不眠や肩こり，抑うつ，頭痛等）を合併することが少なくない。漢方製剤の多くは複数の疾患に対する適応があるので，耳科学的疾患以外の症候に対しても治療が可能な場合があり，有用と考えられる。本総説では耳科学疾患に対する漢方薬を併存症候に注目して整理するとともに，耳科学疾患に対する漢方薬の文献的エビデンスについて解説する。

Speech audiometry is used to measure threshold, to assess suprathreshold intelligibility, to measure progress in lip-reading and auditory training, to detect the presence of malingering, to evaluate the effectiveness of different aids, to predict the success of otologic surgery and to aid in the diagnosis of both peripheral and cortical disorder. They are useful and often essential in modern au...

* Medical Resident Doctor on Otorrhinolaryngology Hospital Professor Edmundo Vasconcelos. ** Fellow Otologic and Skull Base Surgery Universidade de São Paulo. Otorrhinolaryngologist. *** Otorrhinolaryngologist, Hospital Professor Edmundo Vasconcelos. **** Medical Resident Doctor on Otorrhinolaryngology by UNIFESP/EPM. ***** Medical Resident Doctor on Otorrhinolaryngology. ****** Doctor’s Degree...

Stickler's syndrome is an autosomal dominant hereditary condition that presents with pathognomonic facial features, dysplasia, myopia and auditory deficits. This paper describes the auditory history of a family with Stickler's syndrome. Given the expressive variability, a complete audiologic and otologic evaluation is encouraged when Stickler's syndrome is suspected.

Posterior semicircular canal dehiscence is a rare otologic entity that presents with third window signs and symptoms. Petrous apex cholesteatoma, fibrous dysplasia, high riding jugular bulb, and eosinophilic granuloma have been reported to be associated with posterior semicircular canal dehiscence. Here we report a case of development of posterior semicircular canal dehiscence following an endo...

BACKGROUND Atlantoaxial rotatory fixation is a condition in which the first and second vertebrae of the cervical spine become interlocked in a rotated position. This condition can result in serious consequences and thus have a significant impact on patients, especially when diagnosis and treatment are delayed. Some cases of atlantoaxial rotatory fixation have been described in association with ...

BACKGROUND Muckle-Wells-syndrome (MWS) is an autoinflammatory disease characterized by systemic and organ-specific inflammation due to excessive interleukin (IL)-1 release. Inner ear inflammation results in irreversible sensorineural hearing loss, if untreated. Early recognition and therapy may prevent deafness. The aims of the study were to characterize the spectrum of hearing loss, optimize t...