نتایج جستجو برای: primary immunodeficiency disease

تعداد نتایج: 2088150  

Journal: :Clinical infectious diseases : an official publication of the Infectious Diseases Society of America 2014
Jean Gaschignard Corinne Levy Maya Chrabieh Bertrand Boisson Cécile Bost-Bru Stéphane Dauger François Dubos Philippe Durand Joël Gaudelus Dominique Gendrel Christèle Gras Le Guen Emmanuel Grimprel Gaël Guyon Catherine Jeudy Eric Jeziorski Francis Leclerc Pierre-Louis Léger Fabrice Lesage Mathie Lorrot Isabelle Pellier Didier Pinquier Loïc de Pontual Philippe Sachs Caroline Thomas Pierre Tissières Frédéric V Valla Philippe Desprez Véronique Frémeaux-Bacchi Emmanuelle Varon Xavier Bossuyt Robert Cohen Laurent Abel Jean-Laurent Casanova Anne Puel Capucine Picard

BACKGROUND About 10% of pediatric patients with invasive pneumococcal disease (IPD) die from the disease. Some primary immunodeficiencies (PIDs) are known to confer predisposition to IPD. However, a systematic search for these PIDs has never been carried out in children presenting with IPD. METHODS We prospectively identified pediatric cases of IPD requiring hospitalization between 2005 and 2...

2009
Jean-Laurent Casanova Laurent Abel

Despite two decades of mouse immunology and human genetics studies, the pathogenesis of Crohn's disease (CD) remains elusive. New clinical investigations suggest that CD may be caused by inborn errors of macrophages. These errors may result in impaired attraction of granulocytes to the gut wall, causing impaired clearance of intruding bacteria, thereby precipitating the formation of granulomas....

2015
Magda Carneiro-Sampaio Antonio Coutinho

Autoimmune disorders (AID) have been increasingly observed in association with primary immunodeficiencies (PIDs). Here, we discuss the interface between PID and AID, focusing on autoimmune manifestations early in life, which can be diagnostic clues for underlying PIDs. Inflammatory bowel disease in infants and children has been associated with IL-10 and IL-10R deficiencies, chronic granulomatou...

Journal: :Current Opinion in Hematology 2013

Journal: :Proceedings of the Royal Society of Medicine 1975

Journal: :The Journal of clinical investigation 1973
K J Gajl-Peczalska B H Park W D Biggar R A Good

B- and T-cell populations in 32 patients with different forms of primary immunodeficiency disease were studied. The B-cells in peripheral blood were investigated with respect to surface immunoglobulins by means of immunofluorescence. The T-cell function was studied utilizing quantitation of proliferative response to phytochemagglutinin (PHA)(1) and delayed allergy to various antigens. In 10 pat...

2016
Hanne S. Sorte Liv T. Osnes Børre Fevang Pål Aukrust Hans C. Erichsen Paul H. Backe Tore G. Abrahamsen Ole B. Kittang Torstein Øverland Shalini N. Jhangiani Donna M. Muzny Magnus D. Vigeland Pubudu Samarakoon Tomasz Gambin Zeynep H. C. Akdemir Richard A. Gibbs Olaug K. Rødningen Robert Lyle James R. Lupski Asbjørg Stray‐Pedersen

BACKGROUND Four patients from three Norwegian families presented with a common skin phenotype of warts, molluscum contagiosum, and dermatitis since early childhood, and various other immunological features. Warts are a common manifestation of human papilloma virus (HPV), but when they are overwhelming, disseminated and/or persistent, and presenting together with other immunological features, a ...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید