In this paper, we report a case of common pulmonary vein atresia, which is a very rare disease characterized by cyanosis, heart failure and pulmonary hypertension. Reverse flow in the pulmonary artery at end-diastole as well as in the isthmus of the aorta from early systole to end-diastole detected by echocardiography were found to be specific features useful in diagnosing the disease.

The congenital cardiac anomaly known as tetralogy of Fallot (TOF) is characterized by right ventricular outflow tract obstruction caused by subpulmonary stenosis, dextroposition (overriding) of the aorta, a ventricular septal defect, and right ventricular hypertrophy. The right ventricular hypertrophy is secondary to the presence of right ventricular outflow obstruction (pulmonic valvar or subv...

Four patients with tetralogy of Fallot, three of whom had congenital pulmonary atresia, were treated by initial palliative operations to enlarge left and right pulmonary arteries which were considered too small for complete repair. Two to four years later the right and left pulmonary arteries had enlarged sufficiently to allow complete repair.

We analyzed the flow velocity pattern in the main pulmonary artery after Fontan operation in patients with tricuspid atresia (n = 10) or with single ventricle (n = 10) by means of a catheter-mounted velocity probe. The area underneath the velocity signal of the forward flow was integrated, and ratios of the portions during atrial systole and during the diastolic phase to the total area (Fa and ...

Among the cyanotic congenital heart malformations, there is a group characterized anatomically by the presence of an atretic pulmonary artery and a biventricular aorta which acts as the only functioning vessel arising from the heart. A mixture of oxygenated blood from the left ventricle and unsaturated blood from the right ventricle is injected into the aorta, and the pulmonary vessels are fill...

The clinical, pathological, and electrocardiographic findings in congenital pulmonary atresia with intact septum have been reviewed recently by Elliott, Adams, and Edwards (1963). Among their 12 cases, the x-ray examinations on 10 were available for this study. The most characteristic appearance on the frontal chest radiograph in pulmonary atresia is the diminution in the size of the pulmonary ...

the majority of coronary artery fistulas (cafs) are congenital. the anomaly accounts for 0.4% of congenital heart defects and approximately 50% of pediatric coronary vasculature anomalies. twenty percent of people with congenital cafs have other concomitant cardiac anomalies, most frequently aortic and pulmonary atresia and patent ductus arteriosus. it is worthy of note that caf with the tetral...

Sir, In their recent article (1987;57:543-7) on tricuspid atresia with transposition of the great arteries Warnes and Somerville emphasised the inportance of subaortic stenosis in these patients, especially those with coarctation. They suggested that the Fontan procedure was the procedure of choice in these patients but remarked that in patients with subaortic stenosis the prognosis after Fonta...

The patient with complex congenital heart disease, severe pulmonary outflow obstruction, and visceral heterotaxia, may have 'silent' obstruction of the pulmonary venous return. Severe reduction of pulmonary blood flow secondary to pulmonary stenosis or atresia in such patients may prevent the usual radiographic appearance of pulmonary oedema. If such obstructed anomalous pulmonary venous connec...

Mild congenital heart defects require no treatment, while severe forms of these diseases need immediate interventions. There are several limits in preterm neonates on drug interventions, interventional procedures, and even heart surgery due to the prematurity of pulmonary, renal, and central nervous systems. Considering the mentioned points, the collaboration of other medical professions, parti...