OBJECTIVES Type B Niemann-Pick disease (NPD-B) caused by acid sphingomyelinase deficiency is a rare, autosomal recessive, lysosomal storage disorder with a broad range of disease severity. The objectives of this study were to document the natural history of the disease in a large, clinically heterogeneous patient population that was followed for a period of 10 years and to determine how genotyp...

The sulphate radical based advanced oxidation processes (AOPs) are highly in demand these days, owing to their numerous advantages. Herein, the Fe-Mn bimetallic oxide particle was used activate peroxymonosulphate (PMS) for Rhodamine B (RhB) degradation. Three catalysts were synthesized via chemical precipitation method with different concentrations of metals; (1:1), (1:2) and (2:1). best perfor...

AIMS To determine the effects of Mn levels in Bacillus megaterium sporulation and spores on spore resistance. METHODS AND RESULTS Bacillus megaterium was sporulated with no added MnCl(2) and up to 1 mmol l(-1) MnCl(2). The resultant spores were purified and loosely bound Mn removed, and spore Mn levels were found to vary c. 100-fold. The Mn level had no effect on spore γ-radiation resistance,...

Let k ∈ {1, . . . , n}. The k-numerical range of A ∈Mn is the set Wk(A) = {(trX∗AX)/k : X is n× k, X∗X = Ik}, and the k-numerical radius of A is the quantity wk(A) = max{|z| : z ∈ Wk(A)}. Suppose k > 1, k′ ∈ {1, . . . , n′} and n′ < C(n, k)min{k′, n′ − k′}. It is shown that there is a linear map φ : Mn → Mn′ satisfying Wk′(φ(A)) = Wk(A) for all A ∈ Mn if and only if n′/n = k′/k or n′/n = k′/(n−...

Article history:Received 24 June 2008Revised 2 December 2008Accepted 3 December 2008Available online 24 December 2008Hypoxic–ischemic injury (HI) to the neonatal brain results in delayed neuronal death with accompanyinginflammation for days after the initial insult. The aim of this study was to depict delayed neuronal death afterHI using Manganese-enhanced MRI (MEMRI...

In order to obtain accurate information from Internet web pages, a suitable representation of this type of document is required. In this paper, we present the results of evaluating 7 types of web page representations by means of a clustering process. 1 Web Document Representation This work is focused on web page representation by text content. We evaluate 5 representations based solely on the p...

A study was designed to evaluate the micronutrients status of soils of district Palandri, Azad Kashmir and to correlate the micronutrients with Physico-chemical characteristics of soil as well as to categorize the soils as high, medium and low in Cu, Zn, Fe, Mn and HWS B. Soil samples were collected from thirty wheat fields and thirty apple orchard soils during 2003. None of the soil sample was...

The role of bile in manganese metabolism and homeostasis was studied in Holstein bull calves fed diets containing 32 ppm manganese (normal) (control) or 1,000 ppm supplemental manganese (high-manganese) for 2 weeks before and 1 week after intravenous (IV) and duodenal S4Mn dosing. After dosing, all the bile was collected at 15 and 60 minutes, hourly to 12 hr and daily to 7 days. All calves were...