نتایج جستجو برای: brugada syndrome

تعداد نتایج: 622336  

Journal: :Circulation 2001
F Kyndt V Probst F Potet S Demolombe J C Chevallier I Baro J P Moisan P Boisseau J J Schott D Escande H Le Marec

BACKGROUND The SCN5A gene encoding the human cardiac sodium channel alpha subunit plays a key role in cardiac electrophysiology. Mutations in SCN5A lead to a large spectrum of phenotypes, including long-QT syndrome, Brugada syndrome, and isolated progressive cardiac conduction defect (Lenègre disease). METHODS AND RESULTS In the present study, we report the identification of a novel single SC...

Journal: :Annales françaises de médecine d'urgence 2011

Journal: :Circulation Journal 2012

Journal: :Circulation research 2000
M W Veldkamp P C Viswanathan C Bezzina A Baartscheer A A Wilde J R Balser

The congenital long-QT syndrome (LQT3) and the Brugada syndrome are distinct, life-threatening rhythm disorders linked to autosomal dominant mutations in SCN5A, the gene encoding the human cardiac Na(+) channel. It is believed that these two syndromes result from opposite molecular effects: LQT3 mutations induce a gain of function, whereas Brugada syndrome mutations reduce Na(+) channel functio...

2014
Maria Teresa Ricci Silvia Menegon Simona Vatrano Giorgia Mandrile Natascia Cerrato Paula Carvalho Mario De Marchi Fiorenzo Gaita Carla Giustetto Daniela Francesca Giachino

Brugada syndrome is characterised by a typical ECG with ST segment elevation in the right precordial leads. Individuals with this condition are susceptible to ventricular arrhythmias and sudden cardiac death. The principal gene responsible for this syndrome is SCN5A, which encodes the α-subunit of the Nav1.5 voltage-gated sodium channel. Mutations involving other genes have been increasingly re...

Journal: :Journal of the American College of Cardiology 2002
Takashi Kurita Wataru Shimizu Masashi Inagaki Kazuhiro Suyama Atsushi Taguchi Kazuhiro Satomi Naohiko Aihara Shiro Kamakura Junjiro Kobayashi Yoshio Kosakai

OBJECTIVES We sought to demonstrate the electrophysiologic (EP) mechanism of the ST-T change in Brugada syndrome. BACKGROUND Brugada syndrome is characterized by various electrocardiographic manifestations (e.g., right bundle branch block, ST-segment elevation, and terminal T-wave inversion in the right precordial leads) and sudden cardiac death caused by ventricular fibrillation. Direct evid...

Journal: :Europace : European pacing, arrhythmias, and cardiac electrophysiology : journal of the working groups on cardiac pacing, arrhythmias, and cardiac cellular electrophysiology of the European Society of Cardiology 2010
Yukiko Nakano Wataru Shimizu Hiroshi Ogi Kazuyoshi Suenari Noboru Oda Yuko Makita Kenta Kajihara Yukoh Hirai Akinori Sairaku Takehito Tokuyama Yukiji Tonouchi Shigeyuki Ueda Taijiro Sueda Kazuaki Chayama Yasuki Kihara

AIM Risk stratification for Brugada syndrome remains controversial. We investigated the relationships between episodes of ventricular fibrillation (VF) and various clinical, electrocardiographic, electrophysiologic, and genetic parameters both retrospectively and prospectively. METHODS AND RESULTS Fifty-two patients with Brugada syndrome (49 men, average age 42 +/- 3 years) were studied. In t...

2005
Ozcan Ozeke Dursun Aras Bilal Geyik Bulent Deveci Timur Selcuk

ST-segment elevation in Brugada syndrome is caused by a shift in the ionic current balance and the creation of a voltage gradient between the epicardium and the endocardium. This ionic mechanism have been shown to be temperature dependent. We describe a 33-year-old man who presented with fever with the dynamic electrocardiographic changes similar to the Brugada syndrome. These electrocardiograp...

2011
Belinda Sandler Steve Furniss Eric McWilliams

Syncope in a patient with a Brugada syndrome channelopathy carries significant prognostic implications and warrants consideration of implantable cardioverter defibrillator (ICD) implantation. We report a case of a 62-year-old gentleman who presented with a transient loss of consciousness and an electrocardiogram (ECG) suggestive of type 1 Brugada syndrome. Further investigation revealed evidenc...

Journal: :Revista espanola de cardiologia 2005
Berta Daga Antonio Miñano Iris de la Puerta Juana Pelegrín Gonzalo Rodrigo Ignacio Ferreira

Brugada syndrome is characterized by the presence of right bundle branch block on electrocardiography and by ST-segment elevation in the right precordial leads (V1-V3), by the absence of structural cardiac abnormalities, and by episodes of syncope or sudden death. On occasion, diagnosis is made difficult by temporary normalization of the ECG. The condition can be unmasked by potent sodium chann...

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