Cardiac sarcoidosis (CS) is a rare multisystem disorder characterized by granulomatous infiltration of the myocardium, which can lead to significant morbidity and mortality. Its clinical manifestations range from asymptomatic conduction abnormalities severe heart failure (HF) sudden cardiac death. This comprehensive review aims provide an overview diagnosis, features, current medical management...

Pentalogy of Cantrell is a rare congenital abnormality. Even with high-quality medical care and staged corrective surgeries in professional hospitals, the mortality rate still very high long-term prognosis poor. Survival largely determined by complexity severity cardiac abnormalities, efficiency abdominal wall closure postoperative complications. A 24-year-old male patient complete pentalogy wa...

Twenty four patients with ankylosing spondylitis of 10 or more years' duration were assessed for evidence of cardiac disease. Seven patients (29%) had evidence of cardiac disease, including one patient with a pericardial effusion, three with conduction abnormalities, and two with aortic incompetence. Aortic incompetence in one patient was clinically silent and was detected only with Doppler ech...

Abstract Funding Acknowledgements Type of funding sources: None. Background Elevated EFV has been recently reported to be prevalent and a possible contributor higher cardiovascular morbidity mortality, particularly in the presence elevated CACS. Purpose To assess whether CACS significant effects on cardiac electrical activity as evidenced by 12-lead ECG abnormalities, addition triggering inflam...

Objective Noonan syndrome (NS) is a common, autosomal dominant, frequently de novo condition due to mutations in RAS-MAPK pathway genes. Presentation is variable, usually in infancy or early childhood, and includes poor postnatal growth, cardiac abnormalities, dysmorphic features and lymphatic dysplasia. The classic cardiac abnormalities are pulmonary valve dysplasia and hypertrophic cardiomyop...

Isolated left ventricular (LV) apical hypoplasia is a rare congenital cardiac anomaly which is not accompanied by other cardiac abnormalities, with the exception of two cases. We report a case of a 33-year-old male patient with isolated LV apical hypoplasia combined with infundibular pulmonary stenosis and aortic stenosis. We review a literature focusing on the characteristic magnetic resonance...

Results Out of 100 HIV infected children, 42% [25 males, 17 females] had cardiac abnormalities of which only 6 [14%] were symptomatic. Majority belonged to WHO clinical stage IV, with 13 [28%] having low CD4 count. The most common cardiac abnormality was left ventricular systolic dysfunction (LVSD) in 19% (p<0.05). Other abnormalities were mild tricuspid regurgitation in 14%, pericardial effusi...

Cardiac magnetic resonance imaging (CMR) is instrumental in diagnosing myocardial infarction with non-obstructive coronary arteries (MINOCA), allowing exclusion of other aetiologies that are suspected MINOCA—a heterogeneous population. This study investigated the clinical features and outcomes MINOCA patients according to CMR diagnosis: (i) (confirmed infarct), (ii) no abnormalities, (iii) non-...

OBJECTIVES To assess the prevalence and patterns of cardiac abnormalities as detected by cardiac magnetic resonance imaging (MRI) in systemic sclerosis (SSc). METHODS Fifty-two consecutive patients with SSc underwent cardiac MRI to determine morphological, functional, perfusion at rest and delayed enhancement abnormalities. RESULTS At least one abnormality on cardiac MRI was observed in 39/...