نتایج جستجو برای: common variable immunodeficiency cvid
تعداد نتایج: 1013055 فیلتر نتایج به سال:
Background Common Variable Immunodeficiency (CVID) is characterized by reduced serum levels of immunoglobulins (Ig) and its treatment requires regular infusion of intravenous immunoglobulin (IVIG). Eventually CVID female patients will reach reproductive age and it is known that maternofetal transplacental transport of antibodies is important to protect the child in the first months of life. The...
BACKGROUND Common variable immunodeficiency (CVID) is a disorder characterized by hypogammaglobulinemia without a known predisposing cause. CASE PRESENTATION We report a 36-year-old man who had suffered membranoproliferative glomerulonephritis (MPGN) in his childhood, later diagnosed with CVID at 35 years of age. He presented at our hospital with signs of proteinuria. A renal biopsy revealed ...
Common variable immunodeficiency (CVID) is the most frequent clinically expressed primary immunodeficiency in adults and is characterized by primary defective immunoglobulin production. Besides recurrent infectious manifestations, up to 20% of CVID patients develop autoimmune complications. In this study, we took advantages of the French DEFI database to investigate possible correlations betwee...
A patient is reported on with a common variable immunodeficiency syndrome (CVID), in whom chronic gastritis with antibodies against parietal cells and a cytomegalovirus associated enteritis led to vitamin B12 deficiency with consecutive subacute combined degeneration of the spinal cord. The resulting medullary changes, most probably representing demyelination, were visualised with MRI. The effe...
Autoimmune lymphoproliferative disorders, including autoimmune lymphoproliferative syndrome (ALPS) and Dianzani autoimmune lymphoproliferative disease (DALD), are inherited defects of the Fas apoptotic pathway characterized by lymphoid accumulation and autoimmune manifestations. We report the molecular, clinical, immunologic features and the long-term progress of 31 patients. Four carried Fas g...
Background Common Variable Immunodeficiency (CVID) is characterized by hypogammaglobulinaemia and impaired specific antibody production, resulting in increased susceptibility to infections, mainly of the respiratory tract. In an attempt to minimize the recurrent episodes of infections, some studies have recommended immunization with inactivated pathogens or subunits, however, experience with va...
Primary immunodeficiencies (PID) are traditionally considered childhood diseases; however, adults account for 35% of all patients with PID. Antibody deficiencies, especially Common Variable Immunodeficiency (CVID), which have their peak incidence in adulthood, require a high suspicion index. Even though the estimated frequency of CVID is not high (1:25,000), high rates of under diagnosis and un...
common variable immunodeficiency (cvid) is a primary immunodeficiency disease characterized by hypogammaglobulinemia and recurrent bacterial infections especially in respiratory and gastrointestinal systems. we present here 2 cases of cvid with gastrointestinal complications. case 1 is a 25-year-old man with a history of chronic diarrhoea from childhood. ultrasonography revealed ascites, with l...
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BACKGROUND Good syndrome (GS) is a rare condition in which thymoma is associated with hypogammaglobulinemia. It is characterized by increased susceptibility to bacterial, viral, and fungal infections, as well as autoimmunity. Most patients have no circulating B cells. METHODS The French DEFicit Immunitaire de l'adulte cohort provides detailed clinical and immunological descriptions of 690 adu...
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