We reviewed 104 consecutive cases of closed dysraphism in patients seen at one institution between December 1984 and June 1987. All patients had myelographic studies, and 43 had associated CT examinations. Clinical and surgical findings (64 patients) were correlated with myelographic information. Twenty-three patients (22%) with clinical or plain film findings compatible with dysraphism had nor...

INTRODUCTION The aim of this study was to report surgical strategies and clinical outcomes for thoraco-lumbar intradural lipomas. Intraspinal lipomas are rare congenital histologically benign neoplasms, which account for less than 1% of all spinal cord tumors. These tumors are most frequently found in the lumbosacral area as components of a dysraphic state, however, intramedullary lipomas are n...

Delayed and nondelayed bilateral bipedicled fasciocutaneous flaps in large meningomyelocele defects: a preliminary results Congenital fusion defects of the neural tube and the related structures are classified as spinal dysraphism. Meningomyelocele is a defect which is the most common form of spinal dysraphism and occurs at an approximate rate of 1 in 800-1000 live births. In untreated meningom...

Tethered cord syndrome (TCS) or occult spinal dysraphism sequence is a collection of neurological conditions that potentially result from the abnormal fixation of the spinal cord secondary to a developmentally acquired or postoperative pathology. We present a schema for TCS consisting of etiology, embryology, pathophysiology, presentation, and classification in order to facilitate the comprehen...

OBJECTIVES To verify the diagnostic value of lumbosacral midline cutaneous lesions in asymptomatic children to detect occult spinal dysraphism (OSD) and to propose a practical approach for clinical investigations with respect to the type of cutaneous lesions observed. DESIGN Retrospective study of 54 children referred to the Department of Pediatric Dermatology between 1990 and 1999 for congen...

Diphallia is a very rare congenital anomalies occurs 1: 5-6 Million live birth. Associated like imperforate anus, vertebral deformities, double bladder, exstrophy of the cloacae, and duplication recto sigmoid may in association with this. Amongst all anorectal malformations common anomaly that can occur diphallia. Here we are presenting neonate functional penis, partial scrotal dysraphism, high...

Digital techniques are becoming well established as costeffective for vascular imaging in neuroradiology [1, 2]. Pediatric application of this technology is also under development [3]. Futhermore, there has been increasing use of more efficient, less invasive methods of evaluating pediatric spine problems through newer-generation computed tomography (CT), including scanned-projection radiograph...

We explored the prevalence of syringomyelia in a series of 113 cases of fetal dysraphism and hindbrain crowding, of gestational age ranging from 17.5 to 34 weeks with the vast majority less than 26 weeks gestational age. We found syringomyelia in 13 cases of Chiari II malformations, 5 cases of Omphalocele/Exostrophy/Imperforate anus/Spinal abnormality (OEIS), 2 cases of Meckel Gruber syndrome a...