PURPOSE To report an unusual presentation of pellucid marginal degeneration (PMD) and its management by using air injection and tension sutures. CASE REPORT We report 2 cases with a history of acute pain and loss of vision. Examination revealed hydrops at the 6-9 o'clock meridian with Descemet's membrane detachment and tear at the same area and advanced PMD in the other eye. DISCUSSION Air ...

Non-immune hydrops fetalis (NIHF) in a relatively rare syndrome associated with different etiologies, usually due to chromosomal aberrations or cardiac anomalies. Human parvovirus B 19 (HPV B 19) associated intrauterine infections. NIHF and fetal loss have been reported lately. HPV B19 passes through the placenta and infects eiythroid progenitor cells with subsequent lysis, anemia and hydrops. ...

Introduction. Primary congenital lymphedema is a rare disorder associated with insufficient development of lymphatic vessels. Usually most patients present with lower extremity edema seen sonographically. Rarely primary congenital lymphedema may be associated with severe lymphatic dysfunction resulting in hydrops fetalis. Case. A 27-year-old primigravida with a family history of leg swelling th...

Ménière’s disease is a progressive idiopathic disorder that was first described by Prosper Ménière’s . The cause of the disease has not yet been clarified and remains controversial. It is, however, hypothesized that an increased amount of endolymph (endolymphatic hydrops) which causes distension of the endolymphatic sac and the endolymphatic components of the vestibular and cochlear parts may b...

BACKGROUND Keratoconus may progress to acute corneal hydrops even after cross-linking. In some cases, keratoconus progresses during pregnancy. In this report, we present a case of a patient with increased anterior stromal resistance after cross-linking that would favor nonprogression of keratoconus during pregnancy. CASE PRESENTATION We report that cross-linking is likely to have had a protec...

We studied a kindred in which four third-trimester fetal losses occurred, associated with severe Coombs-negative hemolytic anemia and hydrops fetalis. Postmortem examination of two infants revealed extensive extramedullary erythropoiesis. Studies of erythrocytes and erythrocyte membranes from the parents revealed abnormal erythrocyte membrane mechanical stability as well as structural and funct...

We studied a kindred in which four third-trimester fetal losses occurred, associated with severe Coombs-negative hemolytic anemia and hydrops fetalis. Postmortem examination of two infants revealed extensive extramedullary erythropoiesis. Studies of erythrocytes and erythrocyte membranes from the parents revealed abnormal erythrocyte membrane mechanical stability as well as structural and funct...

The association of repeated attacks of vertigo that last for hours with a sense of aural fullness, fluctuating progressive hearing loss and tinnitus is characteristic of endolymphatic hydrops. In most cases, it is impossible to determine an etiology and a diagnosis of idiopathic endolymphatic hydrops, or Ménière’s disease, until it is established. The endolymphatic sac is thought to maintain th...

PURPOSE To report acute corneal hydrops following suture removal after penetrating keratoplasty (PK) in a case of pellucid marginal degeneration (PMD). CASE REPORT A young female underwent PK for corneal scarring in her left eye due to PMD; 8 months later the last sutures were removed. A few days following suture removal, the patient developed acute hydrops in the inferior aspect of the host-...

Generalized lymphatic dysplasia (GLD) is a rare form of primary lymphoedema characterized by a uniform, widespread lymphoedema affecting all segments of the body, with systemic involvement such as intestinal and/or pulmonary lymphangiectasia, pleural effusions, chylothoraces and/or pericardial effusions. This may present prenatally as non-immune hydrops. Here we report homozygous and compound h...