The case is reported of a 41 year old white woman who developed systemic lupus erythematosus (SLE) seven years after primary Sjögren's syndrome and four years after the association of Sjögren's syndrome with Jaccoud's arthritis. The SLE was detected by a benign intracranial hypertension, which is a rare neuro-ophthalmic presentation of lupus. No associated conditions linked to benign intracrani...

The first report of Idiopathic Intracranial Hypertension (IIH) was by Quinche in 1893. Throughout history it has had many names. When I was a child growing up, before we had antibiotic therapy, middle ear infections occasionally would trigger intracranial inflammation and the disease was called Otitic Hydrocephalus. Then it was called Benign Intracranial Hypertension which we now know is far fr...

BACKGROUND Venous sinus disease must be excluded before diagnosing idiopathic intracranial hypertension but is found only rarely in typical cases. Magnetic resonance venography (MRV) is the technique of choice for investigating this, and provides images that are diagnostic and easy to interpret. However, recent work using more invasive techniques has documented pressure gradients and stenoses i...