نتایج جستجو برای: juvenile dermatomyositis

تعداد نتایج: 48304  

Journal: :Seminars in Arthritis and Rheumatism 2018

Background Many pediatric rheumatic diseases persist into adulthood, with negative squeal from the disease or its treatment. We aimed to assess health related quality of life in a group of children with rheumatic diseases and its relation to disease activity and functional disability.  Materials and Methods Fifty one patients were divided into three groups: Group 1 includes 27 patients diagnose...

2016
Satoru Teshigawara Yoshinori Katada Yuichi Maeda Maiko Yoshimura Eriko Kudo-Tanaka Soichiro Tsuji Yoshinori Harada Masato Matsushita Shiro Ohshima Kotaro Watanabe Takahiro Kumode Yoshihiko Hoshida Yukihiko Saeki

BACKGROUND Hemophagocytic lymphohistiocytosis associated with autoimmune diseases is seen in patients with systemic juvenile idiopathic arthritis, adult-onset Still's disease, and systemic lupus erythematosus, whereas it is rarely seen in patients with dermatomyositis. In addition, central nervous system involvement with dermatomyositis is rare. To the best of our knowledge, this is the first c...

Journal: :Statistical methods in medical research 2017
Eh Pieter van Dijkhuizen Claire T Deakin Lucy R Wedderburn Maria De Iorio

Juvenile dermatomyositis is the most common form of the juvenile idiopathic inflammatory myopathies characterised by muscle and skin inflammation, leading to symmetric proximal muscle weakness and cutaneous symptoms. It has a fluctuating course and varying prognosis. In a Bayesian framework, we develop a joint model for four longitudinal outcomes, which accounts for within individual variabilit...

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