Abstract Familial hemophagocytic lymphohistiocytosis (FHL) is a genetically heterogeneous disorder which less typical in adults than pediatric patients. In this study, we reported rare case of adult-onset FHL3 with progressive lymphocytosis and lymphocytic interstitial pneumonia (LIP). A 20-year old female was admitted to our institution for persistent cough fever. chest high-resolution compute...

Abstract Objective Bone grafting is an important surgical procedure to restore missing bone in patients with alveolar cleft lip/palate, aiming stabilize either sides of the maxillary segments by inducing new formation, and bilateral cases also pre-maxilla. Polyphosphate (PolyP), a physiological polymer composed orthophosphate units linked together high-energy phosphate bonds, naturally existing...

A six-month-old girl who presented with dermatitis was found to have multiple, symmetric, deep, gyrate skin folds involving her trunk and similar circumferential lesions on her extremities since birth. She had a characteristic round face with hypertelorism, depressed nasal bridge, thin, down-turned vermillion border of upper lip and short neck. Skin biopsy demonstrated increased smooth muscle f...

A 48 year old woman was referred to hospital for buccal discomfort. Physical examination showed a macroglossia and features of xerostomia. She was diagnosed as having primary Sjögren's syndrome according to the criteria proposed by the European Community study group in 1993. Furthermore, a lower lip salivary gland biopsy showed amyloid deposits that were also seen in the stomach and in the bone...

herein, a 28-year-old man with hoarseness, skin and oral lesions is presented. at the time of admission, the patient had an erythematous plaque on his chin near his lower lip and an erythematous-violaceous plaque on his palate near the open-ing of the pharynx and 20 kg weight lost in last one year. the biopsy of his skin lesions by hematoxylin and eosin staining revealed an infiltration of the ...

one of the most important goals of orthodontic treatment is to create an esthetic, well balanced facial profile. however, the components of a well-balanced iranian facial profile have not yet been established. the purpose of this study was to evaluate the anteroposterior lip position of the iranian population and to compare the perception of orthodontists, dental students and orthodontic patien...

introduction hemangiomas are the most common benign tumor of infancy that can occur anywhere in the body. intramuscular hemangiomas (imh) are accounting for approximately 1% of all cases and the muscles of extremities are the most common sites. because of scarcity and variable clinical features of these tumors, we decided to report a case of imh in the upper lip mucosa. case report the patient ...

background: this study aimed to assess dermis fat graft (dfg) as a choice to correct the tissue deficit in the free border of the upper lip in cleft lip repair surgery. materials and methods: thirty?five individuals who referred to alzahra hospital at 2013–2014,with lip deformity following the primary repair surgery of cleft lip underwent surgery by dfg technique. outcomes were assessed 4 month...

We present a clinical case of primary multiple synchronous highly differentiated keratinizing squamous cell skin cancer in an 84-year old patient with actinic keratosis and cheilitis. The is unique for the simultaneous development carcinoma tip nose vermilion zone lower lip past occupational solar burden, light phenotype, signs chronic photo injury skin. Clinical, dermatoscopic sonographic kera...