BACKGROUND AND PURPOSE There is a scarcity of information on the epidemiology and natural course of moyamoya disease. The aim of this study was to investigate the nationwide epidemiological features of moyamoya disease in Korea, including incidence, prevalence, and survival. METHODS We used the data from nationwide, population-based Health Insurance Review and Assessment Service claims databa...

BACKGROUND Moyamoya is a rare cerebrovascular disease of unknown etiology. The data on moyamoya disease from Pakistan is sparse. We report a case series of 13 patients who presented with moyamoya disease to a tertiary care hospital in Pakistan with a national referral base. METHODS We conducted a retrospective review of thirteen patients who presented to The Aga Khan University and diagnosed ...

BACKGROUND AND PURPOSE Clinical significance of silent microbleeds is unknown in moyamoya disease. This study was aimed to clarify the incidence, locations, and longitudinal course. METHODS This prospective cohort study included 78 nontreated patients with moyamoya disease. The incidence and locations of silent microbleeds were evaluated on T2*-weighted MRI. MR examinations were repeated ever...

BACKGROUND AND PURPOSE Caudate hemorrhage usually results from hypertension, rupture of arteriovenous malformation or aneurysm, or rarely, moyamoya disease. Moyamoya-like changes related to severe atherosclerotic occlusive disease, usually causing ischemic stroke, have been reported. CASE DESCRIPTION A 51-year-old normotensive patient was admitted with headache due to a left caudate hematoma ...

OBJECTIVES Our purpose of this study was to assess the cerebral hemodynamic improvement with perfusion computed tomography (CT), before and after superficial temporal artery (STA) to middle cerebral artery (MCA) bypass surgery in patients with cerebrovascular steno-occlusive diseases including both moyamoya disease and nonmoyamoya steno-occlusions. MATERIALS AND METHODS Twenty-four STA-MCA by...

BACKGROUND AND PURPOSE The progression of occlusive lesions in the major intracranial arteries was believed to be very rare in adult patients with moyamoya disease. The present study aims to clarify the incidence and clinical features of disease progression in adult moyamoya disease. METHODS For the past 15 years, 120 adult Japanese patients were diagnosed with moyamoya disease. Of these, 63 ...

Detection of subtle ischemic injuries in moyamoya disease may enable optimization of timing of revascularization surgery, and could potentially improve functional outcomes. Resting-state functional magnetic resonance imaging (rs-fMRI) is widely used to study functional organization of the brain, but it remains unclear whether rs-fMRI could elucidate distinct characteristics in moyamoya disease....

It is well known that neurofibromatosis is one apparent etiology for the type of intracranial arterial occlusive disease known as moyamoya disease [1-4]. All previously reported cases of neurofibromatosis with moyamoya disease have had involvement only of the intracranial carotid circulation (supraclinoid internal carotid artery, middle cerebral artery, anterior cerebral artery) [1 -4]. We repo...

cerebral stroke is a rare disease in children. moyamoya (mm) is one of the infrequent cerebrovascular diseases with unknown etiology. we report an 8 year-old-boy with chief complain of sudden onset bilateral parietal lobe headache. he mentioned that his headache was first started about three weeks ago and was associated with visual disturbance. his mother declared that the boy developed gait pr...

We conducted a retrospective study to determine whether the presence of moyamoya collaterals influenced the risk of recurrence of cerebrovascular events (CVEs: stroke or transient ischemic attack) in patients with sickle cell disease placed on chronic transfusions after a stroke. Forty-three patients with homozygous sickle cell anemia (HbSS) and 1 with HbSO(Arab) (16 females, 28 males) who had ...