Uterus mullerian adenosarcoma is a very rare malignancy. The clinical and Ultra Sonographic findings are not exclusive and the histomorphologic diagnosis of low-grade adenosarcomas is not straightforward. Herein, we present a young Iranian woman with menometrorrhagia due to exceptional occurrence of uterus Mullerian adenosarcoma. A 24-year-old woman, with menometrorrhagia was referred. Imaging...

A bicornuate uterus is a rare mullerian duct anomaly (MDA) caused by fusion defects of the mullerian duct during embryogenesis.1 They are of clinical significance because they can result in fertility problems ranging from infertility and recurrent abortions to prematurity and malpresentation which increases the perinatal morbidity and mortality rate2. In this paper a case is presented to highli...

Mutations were introduced into conserved steroidogenic factor 1 (SF1)- and SOX9-binding sites within the endogenous mouse Mullerian inhibiting substance (Mis) promoter. Male mice homozygous for the mutant SF1-binding site correctly initiated Mis transcription in fetal testes, although at significantly reduced levels. Surprisingly, sufficient MIS was produced to eliminate the MUllerian ducts. In...

Persistent Mullerian Duct Syndrome (PMDS), a rare form of male pseudohermaphroditism, is characterized by the persistence of Mullerian duct structures (uterus, fallopian tubes and upper two-thirds of vagina) in otherwise normallyvirilized males (Karyotype 46XY). Patients suffering from PMDS present with cryptorchidism, inguinal hernia and infertility. Diagnosis is established when Mullerian duc...

Only five cases of recurrence of malignant mixed Mullerian tumor (carcinosarcoma) from the ovarian carcinoma have been published in the literature to our knowledge. A 64-year-old woman first underwent a total abdominal hysterectomy and bilateral salpingo-oophorectomy because of pelvic mass. Histological diagnosis was serous papillary carcinoma of the left ovary. After six courses of chemotherap...

INTRODUCTION Persistent Mullerian duct syndrome (PMDS) is a rare type of pseudohermaphroditism in genotypically and phenotypically males. They have a uterus, fallopian tubes, and upper part of the vagina; but Mullerian duct fails to regress. In transverse testicular ectopia (TTE), one of the testis moves to the opposite side and both testes pass the same inguinal canal. We report a case of PMDS...

The Herlyn-Werner-Wunderlich syndrome (OHVIRA syndrome) is a rare urogenital malformation, characterized by blind hemivagina, didelphic uterus, and homolateral renal agenesis, it results from defect in the development of muller Wolf ducts during embryonic period, unknown origin, diagnosis most often made at puberty first menstruation, sometimes late, particularly for non-obstructive forms: infe...

Mullerian adenosarcoma of the cervix is a rare tumor composed of benign epithelial and malignant stromal components. Sarcomatous overgrowth and heterologous elements in cervical adenosarcoma are extremely infrequent. We report the case of a 26-year-old woman admitted at the gynaecology department for a painless mass protruding from her vagina. The initial pathological exam concluded to endocerv...

Introduction/Background The aim of this study is to evaluate the accuracy three-dimensional transvaginal ultrasound (3D-TVS) for diagnosis uterine mullerian anomalies (UMA), using surgery as reference standard. Methodology A search was performed in PubMed/MEDLINE, CINAHL, Scopus, Cochrane and Web Science databases (January 1990 December 2021) studies evaluating diagnostic perf...

Abstract Background Mullerian duct anomalies are a broad spectrum of congenital the female genital tract presenting with variable symptoms like infertility, amenorrhoea, dysmenorrhea, pelvic endometriosis, and poor obstetric outcomes. Unicornuate uterus or hemiuterus occurs as result abnormal formation failure contralateral part. Case presentation We present rare case report functional non-comm...