نتایج جستجو برای: neurometabolic disorders

تعداد نتایج: 671446  

Journal: :iranian journal of child neurology 0
parvaneh karimzadeh 1. pediatric neurology research center, shahid beheshti university of medical sciences, tehran, iran 2. pediatric neurology center of excellence, department of pediatric neurology, mofid children hospital, faculty of medicine, shahid beheshti university of medical sciences, tehran, iran narjes jafari 1. pediatric neurology research center, shahid beheshti university of medical sciences, tehran, iran 2. pediatric neurology center of excellence, department of pediatric neurology, mofid children hospital, faculty of medicine, shahid beheshti university of medical sciences, tehran, iran habibe nejad biglari 1. pediatric neurology research center, shahid beheshti university of medical sciences, tehran, iran sayena jabbehdari 1. pediatric neurology research center, shahid beheshti university of medical sciences, tehran, iran 6. students’ research committee, faculty of medicine, shahid beheshti university of medical sciences, tehran, iran mehdi alizadeh 3. pediatrician, mahneshan razi general hospital, zanjan medical university of medical sciences, zanjan, iran ghazal alizadeh 1. pediatric neurology research center, shahid beheshti university of medical sciences, tehran, iran

how to cite this article: karimzadeh p, jafari n, nejad biglari hb, jabbehdari s, alizadeh m, alizadeh gh, nejad biglari hm, sanii s. the clinical features and diagnosis of adrenoleukodystrophy: a case series of iranian family. iran j child neurol. winter 2016; 10(1):61-64. abstract objective adrenoleukodystrophy disorder is one of the x-linked genetic disorders caused by the myelin sheath brea...

Journal: :Molecular genetics and metabolism 2011
Sarah Mangold Nenad Blau Thomas Opladen Robert Steinfeld Britta Wessling Klaus Zerres Martin Häusler

BACKGROUND Cerebral folate deficiency (CFD) is increasingly recognized in various neurological conditions, raising the question of whether it might represent a clear-cut clinical syndrome. METHODS Retrospective analysis of patients with low cerebral spinal fluid (CSF) 5-methyltetrahydrofolate (5MTHF) values was performed. RESULTS 58 pediatric patients with low (-2nd to -3rd standard deviati...

2016
Linda Cassis Elisenda Cortès-Saladelafont Marta Molero-Luis Delia Yubero Maria Julieta González Aida Ormazábal Carme Fons Cristina Jou Cristina Sierra Esperanza Castejon Ponce Federico Ramos Judith Armstrong M. Mar O’Callaghan Mercedes Casado Raquel Montero Silvia Meavilla-Olivas Rafael Artuch Ivo Barić Franco Bartoloni Cinzia Maria Bellettato Fedele Bonifazi Adriana Ceci Ljerka Cvitanović-Šojat Christine I. Dali Francesca D’Avanzo Ksenija Fumic Viviana Giannuzzi Christina Lampe Maurizio Scarpa Ángels Garcia-Cazorla

Linda Cassis, Elisenda Cortès-Saladelafont, Marta Molero-Luis, Delia Yubero, Maria Julieta González, Aida Ormazábal, Carme Fons, Cristina Jou, Cristina Sierra, Esperanza Castejon Ponce, Federico Ramos, Judith Armstrong, M. Mar O’Callaghan, Mercedes Casado, Raquel Montero, Silvia Meavilla-Olivas, Rafael Artuch, Ivo Barić, Franco Bartoloni, Cinzia Maria Bellettato, Fedele Bonifazi, Adriana Ceci, ...

2001
Sergio E. Starkstein Janus L. Kremer

The aging process is associated with a progressive cognitive decline, but both the extent of this decline and the profile of age-related cognitive changes remain to be clearly established. Currently, cognitive deficits associated with aging may be diagnosed under the categories of age-associated memory impairment, age-associated cognitive impairment, or the Diagnostic and Statistical Manual of ...

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