نتایج جستجو برای: pseudohypoaldosteronism type 1

تعداد نتایج: 3647227  

Journal: :Clinical medicine & research 2003
Friedrich C Luft

Mendelian forms of hypertension have ushered in a revolution in our knowledge of blood pressure and volume regulation. If we include information on syndromes involving low blood pressure, this knowledge base is doubled. Glucocorticoid remediable aldosteronism, apparent mineralocorticoid excess, and mutations in the mineralocorticoid receptor gene have given us brilliant insights into mineraloco...

Journal: :The Journal of biological chemistry 2008
Min Lu Fernando Echeverri Dalia Kalabat Bianca Laita David S Dahan Raymond D Smith Hong Xu Lena Staszewski Jeff Yamamoto Jing Ling Nancy Hwang Rachel Kimmich Peter Li Erika Patron Walter Keung Andrew Patron Bryan D Moyer

The epithelial sodium channel (ENaC), a heterotrimeric complex composed of alpha, beta, and gamma subunits, belongs to the ENaC/degenerin family of ion channels and forms the principal route for apical Na(+) entry in many reabsorbing epithelia. Although high affinity ENaC blockers, including amiloride and derivatives, have been described, potent and specific small molecule ENaC activators have ...

Journal: :Physical review letters 2004
Florian R Krajewski Martin H Müser

Discrete sine-Gordon (SG) chains are studied with path-integral molecular dynamics. Chains commensurate with the substrate show the transition from pinning to quantum creep at bead masses slightly larger than in the continuous SG model. Within the creep regime, a field-driven transition from creep to complete depinning is identified. The effects of disorder on the chain's dynamics depend on the...

Journal: :acta medica iranica 0
a. rabbani. b. goharfar a. dehgani

- pseudohypoaldosteronism (p'ha) is referred to a state of endorgan unresponsiveness to aldosterone. in this article a 12 day - old mule newborn is presented with hyponatremia, hyperkalemia and metabolic acidosis. aldosterone level and plasma renin activity were high. mineralocorticoids had no therapeutic effect, hut normal saline infusion improved electrolyte imbalance. salt-rich diet was succ...

2015
Frances-Rose Schumacher Keith Siew Jinwei Zhang Clare Johnson Nicola Wood Sarah E Cleary Raya S Al Maskari James T Ferryman Iris Hardege Nichola L Figg Radoslav Enchev Axel Knebel Kevin M O’Shaughnessy Thimo Kurz

Deletion of exon 9 from Cullin-3 (CUL3, residues 403-459: CUL3(Δ403-459)) causes pseudohypoaldosteronism type IIE (PHA2E), a severe form of familial hyperkalaemia and hypertension (FHHt). CUL3 binds the RING protein RBX1 and various substrate adaptors to form Cullin-RING-ubiquitin-ligase complexes. Bound to KLHL3, CUL3-RBX1 ubiquitylates WNK kinases, promoting their ubiquitin-mediated proteasom...

2006
R. Chacón

Spatiotemporal chaos arising from the competition between sine-Gordonbreather and kink-antikink-pair solitons by reshaping an ac force is demonstrated. After introducing soliton collective coordinates, Melnikov’s method is applied to the resulting effective equation of motion to estimate the parameterspace regions of the ac force where homoclinic bifurcations are induced. The analysis reveals t...

Journal: :Optics express 2008
W Shieh H Bao Y Tang

Coherent optical OFDM (CO-OFDM) has recently been proposed and the proof-of-concept transmission experiments have shown its extreme robustness against chromatic dispersion and polarization mode dispersion. In this paper, we first review the theoretical fundamentals for CO-OFDM and its channel model in a 2x2 MIMO-OFDM representation. We then present various design choices for CO-OFDM systems and...

Journal: :Journal of marriage and the family 2013
Frank D Fincham Ming Cui Mellissa Gordon Koji Ueno

In our article, ‘‘The Continuation of Intimate Partner Violence from Adolescence to Young Adulthood’’ (Cui, Ueno, Gordon, & Fincham, 2013), we found that being victimized by relationship partners in adolescence was significantly associated with both perpetration and victimization in romantic relationships in young adulthood. Though not our primary focus, we included gender as a covariate and te...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید