The urea cycle functions to incorporate ammonia, generated by normal metabolism, into urea. Urea cycle disorders (UCDs) are caused by loss of function in any of the enzymes responsible for ureagenesis, and are characterized by life-threatening episodes of acute metabolic decompensation with hyperammonemia (HA). A prospective analysis of interim HA events in a cohort of individuals with ornithin...

The composite flour was produced with wheat flour, sweet potato chick pea and soybean (WF:SPF:CPF:SF) in the proportions of 100:0:0:0 (control), 0:100:0:0 (100% SPF), 70:10:10:10 (10% 60:20:10:10 (20% 50:30:10:10 (30% 40:40:10:10 (40% 30:50:10:10 (50% 20:60:10:10 (60% 10:70:10:10 (70% SPF). addition SPF blends leads to elevation fiber, ash, minerals, bioactive components. Protein content increa...

Superplastic forming (SPF) is introduced in this article as a net-shape processing method for bulk metallic glasses (BMGs), commercially known as Liquidmetal® alloys. This method decouples fast cooling and forming of the BMG. Forming takes place in the supercooled liquid region, where the BMG exists as a highly viscous liquid and increases its fl uidity with increasing temperature. The SPF meth...

Existing process mining techniques provide summary views of the overall process performance over a period of time, allowing analysts to identify bottlenecks and associated performance issues. However, these tools are not designed to help analysts understand how bottlenecks form and dissolve over time nor how the formation and dissolution of bottlenecks – and associated fluctuations in demand an...

In this paper, we report our experimental study on directly coupling a micro/nano fiber (MNOF) ring with a side-polished fiber(SPF). As a result of the study, the behavior of an add-drop filter was observed. The demonstrated add-drop filter explored the wavelength dependence of light coupling between a MNOF ring and a SPF. The characteristics of the filter and its performance dependence on the ...

The sparse-fur (spf) mutant mouse has an X-linked deficiency of hepatic ornithine transcarbamylase (OTC), and devetops hyperftmmonemia immediately after weaning and maintains it throughout its life span. We haye studied the effects of acetyl-L-carnitine (ALCAR) on the hepatic mitochondrial proteins of the chronicaJly hyperammonemic spf mice. Two different age groups of mice were studied, the we...

We propose a multi-shell sampling grid and develop corresponding transforms for the accurate reconstruction of the diffusion signal in diffusion MRI by expansion in the spherical polar Fourier (SPF) basis. The transform is exact in the radial direction and accurate, on the order of machine precision, in the angular direction. The sampling scheme uses an optimal number of samples equal to the de...

This research developed the Scale of Protective Factors (SPF-24) to measure protective factors contributing to resilience. We investigated the factor structure of 35 items. After exploratory factor analysis, we subjected 25 items representing 2 social-interpersonal and 2 cognitive-individual factors to confirmatory factor analysis. The sample consisted of 942 college students from 3 studies and...

Mice with the X-chromosomal sparse-fur (spf) mutation frequently have urinary bladder stones composed mostly of orotic acid, which was identified by the following criteria: ultraviolet and infrared absorption, spectra, chromatographic behavior, melting point, and reactivity in a specific color test. This clue led to the discovery that spf-bearing mice have an abnormal form of liver ornithine ca...