A 25 year old male and his 46 year old aunt presented with shortness of breath and a dramatic response to steroids. The other two patients are sisters with more advanced disease. One of these responded partially to steroids, while the other died within 4 months of treatment. The genetic basis and pathogenesis are discussed.

PURPOSE The results of steroid withdrawal in pancreas transplant recipients under tacrolimus immunosuppression were analyzed. METHODS From July 4, 1994 until April 30, 1998, 147 pancreas transplantations were performed in 141 patients, including 126 simultaneous pancreas-kidney transplantations, 13 pancreas after kidney transplantation, and 8 pancreas transplantations alone. Baseline immunosu...

Recently, the use of sport supplements has become so common among most athletes. These supplements may contain undeclared substances that are banned by such international authorities as WHO, IOC and WADA. The present study, thus, is aimed at examining the final sport supplement products in terms of banned substances and measuring the adulteration level in order to prove the safety of these prod...

The inhibitory effects of several steroids on G6PD activity using intact erythrocytes are reported. Incubation of whole blood with dehydroepiandrosterone (DHEA) resulted in 42% and 12% inhibition in the enzyme activity in the presence and absence of oxygen, respectively. Addition of epinephrine and/or aminophylline into the incubation medium caused further enzyme inhibition suggesting a po...

Since the introduction of inhaled steroids for the treatment of asthma, numerous studies have shown that they have an advantageous therapeutic index in relation to oral steroids, as well as high potency. They certainly represent a major 3:dvance in asthma treatment. Initially, inhaled steroids were used in moderate doses and primarily as a substitute for oral steroids. In recent years we have s...

the inhibitory effects of several steroids on g6pd activity using intact erythrocytes are reported. incubation of whole blood with dehydroepiandrosterone (dhea) resulted in 42% and 12% inhibition in the enzyme activity in the presence and absence of oxygen, respectively. addition of epinephrine and/or aminophylline into the incubation medium caused further enzyme inhibition suggesting a possibl...

Elective tonsillectomy remains one of the most commonly performed operations in otolaryngology, with postoperative hemorrhage (PTH) being the most significant potential complication. Anecdotal evidence among ENT Surgeons suggested that bodybuilding athletes may be at increased risk of suffering from PTH, a notion corroborated by a recent case report, regarding primary PTH. The problem has been ...