Persistent left superior vena cava is the most common form of anomalous venous drainage involving the superior vena cava, and represents persistence of the left horn of the embryonic sinus venosus, which normally involutes during normal development to become the coronary sinus. Almost always, a persistent left superior vena cava enters the right atrium through the orifice of an enlarged coronar...

Venous aneurysms arising from the mediastinal systemic veins are rare. There are only 27 reported cases of such aneurysms. Majority arise from the superior vena cava. We are reporting a saccular aneurysm of superior vena cava in a 58-year-old male. The chest radiogram suggested superior mediastinal mass and the computed tomogram was suggestive of aortic arch aneurysm. Aortography and venography...

The benefits of a baffle fenestration in essentially high-risk Fontan patients have been demonstrated. Described here is the use of a new fenestration between the left atrial appendage and the left superior vena cava after Kawashima operation in a patient with a double-outlet right ventricle with hypoplastic left ventricle, left atrial isomerism, bilateral superior vena cavae with no bridging v...

The majority of patients requiring pacemakers are paced using a transvenous electrode. Difficulties may be encountered in passing the electrode wire into the heart because of anomalous venous return. Probably the most frequent anomaly is a persistent left superior vena cava and the rarest is absence of the right superior vena cava (Winter, 1954; Hudson, I965; Sherman, I963). Recent case reports...

Pseudoaneurysm of the right ventricular outflow tract (RVOT) has been reported as a rare complication of RVOT reconstruction performed using conduit replacement or patch repair. Rarely, it may present alongside symptoms secondary to the compression of adjoining mediastinal structures. We report the case of a patient who developed a symptomatic RVOT pseudoaneurysm one month after a total correct...

Two patients with transvenous permanent pacemakers developed thrombosis and occlusion of the superior vena cava around a broken pacing wire, with clot extending into the innominate, subclavian, and axillary veins. Both patients had symptoms and signs of the superior vena cava syndrome which failed to resolve despite anticoagulant and thrombolytic treatment. Obstruction to venous flow, however, ...

A patient with a bi-atrial-ventricular permanent pacemaker due to paroxystic atrial fibrillation associated to sinus bradycardia, in chronic use of oral anticoagulant, presented clinical signs of superior vena cava syndrome. Digital subtraction venography showed total obstruction of the right brachiocephalic venous trunk and severe stenosis of the connection of the left trunk to the superior ve...

Coronary sinus anomalies are rare congenital defects which are usually coexistent with a persistent left superior vena cava and may be associated with cardiac arrhythmias. We report an unroofed coronary sinus without persistent left superior vena cava diagnosed during a catheter ablation procedure for Wolff-Parkinson-White syndrome. Diagnostic and therapeutic options and outcomes are discussed....

We herein report a case of fetal long QT syndrome with a series of cardiac arrhythmias resulting from a 2:1 atrioventricular block and high grade atrioventricular block with polymorphic ventricular premature contractions leading to ventricular tachycardia. These were detected in late gestation using the M-mode and simultaneous Doppler flow recording of the superior vena cava and the ascending a...