نتایج جستجو برای: vertical coplanar vcp

تعداد نتایج: 99181  

2012
Mário N. Laço Luisa Cortes Sue M. Travis Henry L. Paulson A. Cristina Rego

Alterations in the ubiquitin-proteasome system (UPS) have been reported in several neurodegenerative disorders characterized by protein misfolding and aggregation, including the polylgutamine diseases. Machado-Joseph disease (MJD) or Spinocerebellar Ataxia type 3 is caused by a polyglutamine-encoding CAG expansion in the ATXN3 gene, which encodes a 42 kDa deubiquitinating enzyme (DUB), ataxin-3...

2012
Marie-Noëlle Laguë Raphaëlle Romieu-Mourez Éric Bonneil Alexandre Boyer Nicolas Pouletty Anne-Marie Mes-Masson Pierre Thibault Marie-Ève Nadeau Derek Boerboom

The initial aim of this study was to identify novel serum diagnostic markers for the human ovarian granulosa cell tumor (GCT), a tumor that represents up to 5% of all ovarian cancers. To circumvent the paucity of human tissues available for analyses, we used the Ctnnb1(tm1Mmt/+);Pten(tm1Hwu/tmiHwu);Amhr2(tm3(cre)Bhr/+) transgenic mouse model, which features the constitutive activation of CTNNB1...

Journal: :Cancer research 2005
Mark Livingstone Hong Ruan Jessica Weiner Karl R Clauser Peter Strack Shengfang Jin Amy Williams Heidi Greulich James Gardner Monica Venere Tamara A Mochan Richard A DiTullio Katarina Moravcevic Vassilis G Gorgoulis Anne Burkhardt Thanos D Halazonetis

The response of eukaryotic cells to DNA damage includes the activation of phosphatidylinositol-3 kinase-related kinases (PIKK), such as ATM, ATR, and DNA-dependent protein kinase (DNA-PK). These three kinases have very similar substrate specificities in vitro, but in vivo, their substrates overlap only partially. Several in vivo substrates of ATM and ATR have been identified and almost all of t...

2015
Katrina J. Llewellyn Naomi Walker Christopher Nguyen Baichang Tan Lbachir BenMohamed Virginia E. Kimonis Angèle Nalbandian Udai Pandey

The discovery of effective therapies and of disease mechanisms underlying valosin containing protein (VCP)-associated myopathies and neurodegenerative disorders remains elusive. VCP disease, caused by mutations in the VCP gene, are a clinically and genetically heterogeneous group of disorders with manifestations varying from hereditary inclusion body myopathy, Paget's disease of bone, frontotem...

Journal: :Cell 2001
Krishna H.M Murthy Scott A Smith Vannakambadi K Ganesh Ken W Judge Nick Mullin Paul N Barlow Craig M Ogata Girish J Kotwal

Vaccinia virus complement control protein (VCP) inhibits both pathways of complement activation through binding the third and fourth components. A homolog of mammalian regulators of complement activation, its ability to bind heparin endows VCP with additional activities of significance to viral infectivity. The structure of VCP reveals a highly extended molecule with a putative heparin recognit...

2005
Nihad Dib

In this article, a new CAD model for the coplanar waveguide (CPW) cross-over air-bridge is proposed. The model takes into account the CPW open-end capacitance and the vertical strips of the bridge. The section directly underneath the bridge is modeled as a small section of a microstrip line. Our results are in good agreement with the published full-wave results. © 2005 Wiley Periodicals, Inc. I...

2017
Ning Zhou Ben Ma Shaunrick Stoll Tristan T. Hays Hongyu Qiu

Hypertension-induced left ventricular hypertrophy (LVH) is an independent risk factor for heart failure. Regression of LVH has emerged as a major goal in the treatment of hypertensive patients. Here, we tested our hypothesis that the valosin-containing protein (VCP), an ATPase associate protein, is a novel repressor of cardiomyocyte hypertrophy under the pressure overload stress. Left ventricul...

2016
S Figueroa-Bonaparte J Hudson R Barresi T Polvikoski T Williams A Töpf E Harris D Hilton-Jones R Petty T A Willis C Longman C F Dougan M J Parton M G Hanna R Quinlivan M E Farrugia M Guglieri K Bushby V Straub H Lochmüller T Evangelista

INTRODUCTION Hereditary inclusion body myopathy (IBM) with Paget’s disease of the bone (PDB) and frontotemporal dementia (FTD) (IBMPFD) is a rare autosomal dominant disorder due to mutations in the valosin-containing protein gene (VCP). Pathogenic VCP variants have also been associated with amyotrophic lateral sclerosis and other phenotypes including dilated cardiomyopathy and Parkinson’s disea...

Journal: :Journal of medical robotics research 2021

Previously, a pneumatic design of fingertip haptic device (FHD) was developed for virtual reality applications. In this paper, the feasibility representing tissues varying stiffness is investigated. Physical properties, and Young’s modulus variable compliance platform (VCP) were compared with set bolus materials soft tissues. moduli ten times higher than those from VCP, whereas fairly similar. ...

Journal: :Journal of immunology 2010
Yuming Guo Jun Chen Lei Shi Zusen Fan

Granzyme K (GzmK) highly expressed in NK and NKT cells. We recently demonstrated that GzmK induces rapid caspase-independent cell death with ssDNA nicks. Little is known about its molecular mechanisms to mediate caspase-independent cell death. In this study, we found the valosin-containing protein (VCP) is a physiological substrate of GzmK. GzmK cleaves VCP at residue Arg(713) in the D2 domain ...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید