نتایج جستجو برای: mismatch repair system

تعداد نتایج: 2365354  

2015
Ke Xu A. Francis Stewart Andrew C.G. Porter

The correction of disease-causing mutations by single-strand oligonucleotide-templated DNA repair (ssOR) is an attractive approach to gene therapy, but major improvements in ssOR efficiency and consistency are needed. The mechanism of ssOR is poorly understood but may involve annealing of oligonucleotides to transiently exposed single-stranded regions in the target duplex. In bacteria and yeast...

Journal: :Genetics 1999
K J Hillers F W Stahl

In Saccharomyces cerevisiae, some gene loci manifest gradients in the frequency of aberrant segregation in meiosis, with the high end of each gradient corresponding to a hotspot for DNA double-strand breaks (DSBs). The slope of a gradient is reduced when mismatch repair functions fail to act upon heteroduplex DNA-aberrant segregation frequencies at the low end of the gradient are higher in the ...

Journal: :Haematologica 2010
Tim Ripperger Carmela Beger Nils Rahner Karl W Sykora Clemens L Bockmeyer Ulrich Lehmann Hans H Kreipe Brigitte Schlegelberger

Biallelic mutations of mismatch repair genes cause constitutional mismatch repair deficiency associated with an increased risk for childhood leukemia/lymphoma. We report on a case with constitutional mismatch repair deficiency caused by a novel MSH6 mutation leading to a T-cell lymphoma and colonic adenocarcinoma at six and 13 years of age, respectively. A review of the literature on hematologi...

Journal: :Cancer research 2003
Liang Wang Julie M Cunningham Jennifer L Winters Jennifer C Guenther Amy J French Lisa A Boardman Lawrence J Burgart Shannon K McDonnell Daniel J Schaid Stephen N Thibodeau

Frequent BRAF mutations were reported recently in a variety of human malignancies, including colorectal cancer. In this study, we screened 293 colorectal cancers for mutations in exons 11 and 15, two regions containing hotspots for BRAF mutation. Of the 293 cancers, 170 had normal mismatch repair, and 123 had defective mismatch repair (originating from both somatic as well as germ-line mutation...

2014
Patrick Joost Nynke Veurink Susanne Holck Louise Klarskov Anders Bojesen Maria Harbo Bo Baldetorp Eva Rambech Mef Nilbert

BACKGROUND Immunohistochemical staining for mismatch repair proteins is efficient and widely used to identify mismatch repair defective tumors. The tumors typically show uniform and widespread loss of MMR protein staining. We identified and characterized colorectal cancers with alternative, heterogenous mismatch repair protein staining in order to delineate expression patterns and underlying me...

2018
Karl P Hodel Richard de Borja Erin E Henninger Brittany B Campbell Nathan Ungerleider Nicholas Light Tong Wu Kimberly G LeCompte A Yasemin Goksenin Bruce A Bunnell Uri Tabori Adam Shlien Zachary F Pursell

Tumors defective for DNA polymerase (Pol) ε proofreading have the highest tumor mutation burden identified. A major unanswered question is whether loss of Pol ε proofreading by itself is sufficient to drive this mutagenesis, or whether additional factors are necessary. To address this, we used a combination of next generation sequencing and in vitro biochemistry on human cell lines engineered t...

Journal: :Genetics 1999
Y Xie C Counter E Alani

The RFC1 gene encodes the large subunit of the yeast clamp loader (RFC) that is a component of eukaryotic DNA polymerase holoenzymes. We identified a mutant allele of RFC1 (rfc1::Tn3) from a large collection of Saccharomyces cerevisiae mutants that were inviable when present in a rad52 null mutation background. Analysis of rfc1::Tn3 strains indicated that they displayed both a mutator and repea...

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