Peripheral facial nerve paralysis is relatively common in the pediatric age group. Infectious agents convincingly associated with acute facial palsy include varicella-zoster virus, herpes simplex virus, cytomegalovirus, Epstein–Barr virus, rubella virus, and more recently, human immunodeficiency virus. However, facial palsy has rarely been documented in patients with mumps virus infection. Faci...

BACKGROUND Primary periodic paralyses are rare inherited muscle diseases characterised by episodes of flaccid weakness affecting one or more limbs, lasting several hours to several days, caused by mutations in skeletal muscle channel genes. OBJECTIVES The objective of this review was to systematically review treatment of periodic paralyses. SEARCH STRATEGY We searched the Cochrane Neuromusc...

BACKGROUND Mycosis fungoides and Sézary syndrome are cutaneous T-cell lymphomas characterized by the epidermotropism of tumor cells. Neuropathic disease is rare during mycosis fungoides and Sézary syndrome and usually results from a central nervous system involvement in late stages. Neurolymphomatosis is defined as the infiltration of the peripheral nerves by tumor lymphocytes. It has been desc...

Contrast sensitivity for face identification was measured as a function of image size to find out whether foveal and peripheral performance would become equivalent by magnification. Size scaling was not sufficient for this task, but when the data was scaled both in size and contrast dimensions, there was no significant eccentricity-dependent variation in the data, i.e. for equivalent performanc...

Familial amyloid polyneuropathy (FAP) type IV (FINNISH) is a rare clinical entity with challenging neuropathy and cosmetic deficits. Amyloidosis can affect peripheral sensory, motor, or autonomic nerves. Nerve lesions are induced by deposits of amyloid fibrils and treatment approaches for neuropathy are challenging. Involvement of cranial nerves and atrophy in facial muscles is a real concern i...

This review of the primary familial periodic paralyses (PFPP) summarizes the pertinent clinical and laboratory findings of the three forms of this dis­ order. The review is intended to highlight diagnostic features of PFPP and to discuss current hypotheses regarding pathogenesis.

OBJECTIVES To develop a mouse model for measuring facial nerve injury and recovery and to test the hypothesis that overexpression of the antiapoptotic gene, bcl2, enhances recovery of facial nerve function after peripheral crush injury. DESIGN Prospective analysis of recovery of function after facial nerve crush injury in mice at juvenile (postnatal day 7) and adult (postnatal day 30) ages wi...

Neurological complications are important causes of morbidity and mortality in patients with human immunodeficiency virus (HIV) infection. They can occur at any stage of the disease and can affect any level of the central or peripheral nervous systems. In the literature, several cases of HIV-associated facial paralysis have been reported; however, bilateral facial palsy is rarely reported. In th...

Ramsay Hunt syndrome (RHS) is characterized by facial paralysis, inner ear dysfunction, periauricular pain, and herpetiform vesicles. The reported incidence in children is 2.7/100,000. The pathogenesis involves the reactivation of latent varicella zoster virus (VZV) in the geniculate ganglion of the facial nerve. The recovery rate is better in children than in adults. This paper discusses a 12-...