نتایج جستجو برای: pick c

تعداد نتایج: 1066027  

Journal: :Journal of neurology, neurosurgery, and psychiatry 2003
K A Josephs M W Van Gerpen J A Van Gerpen

Niemann-Pick disease type C (NPC) is an autosomal recessive neurometabolic disorder that rarely presents in adulthood, and is associated with cognitive decline, various movement disorders (ataxia, chorea, dystonia, and myoclonus), a vertical supranuclear gaze palsy (VSGP), and seizures. A recent case report demonstrated a delay in diagnosis of eight years when a patient with NPC presented with ...

Journal: :World journal of pediatrics : WJP 2012
Hui Xiong Xin-Hua Bao Yue-Hua Zhang You-Ning Xu Jiong Qin Hui-Ping Shi Xi-Ru Wu

BACKGROUND Niemann-Pick disease type C (NP-C), derived from mutation of the NPC1 or NPC2 gene, is one of the recessive lysosomal lipid storage disorders that are difficult to diagnose and treat. Since NP-C has been rarely reported in China, we reviewed 7 patients with NP-C. METHODS The 7 patients had been diagnosed with NP-C from 2007 to 2010 at our department and their laboratory and clinica...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید