I. Endo M, Takayasu S, Obunai Y, Nakazawa M, Konno S: Anomalous origin of left coronary artery from pulmonary artery. Significance of saphenous vein bypass between aorta and left coronary artery. J Thorac Cardiovasc Surg 67: 896, 1974 2. Anthony CL Jr, McAllister HA Jr, Cheitlin MD: Spontaneous graft closure in anomalous origin of the left coronary artery. Chest 68: 586, 1975 3. Askenazi J, Nad...

A 72-year-old man presented with right-sided pleuritic chest pain, chronic cough and weight loss. Chest x ray revealed a moderate sized pleural effusion. Chest CT showed thromboem-bolism of the right main pulmonary artery, and pleural effusion with compression atelactasis of the right lower lobe of the lung (fig 1). As the thrombus appeared suspicious, being unilateral, central and occupying th...

Connective Tissue Disease (CTD) is an autoimmune disease involving connective tissues, including sjogren syndrome (pSS), rheumatoid arthritis (RA), systemic sclerosis (SSc), mixed tissue (MCTD), lupus erythematosus (SLE), etc. [1,2]. Pulmonary Arterial Hypertension (PAH) refers to a pathological condition in which the pulmonary artery pressure rises above certain threshold, causing right heart ...

We describe our experience with a patient who had metastasized pulmonary artery sarcoma, but survived 7 years after diagnosis. A 61-year-old man was diagnosed with pulmonary artery intimal sarcoma after resection of metastatic tumours to the bilateral lungs. The primary lesion in the pulmonary artery trunk extending into the bilateral branches was treated by tumour endoarterectomy followed by c...

BACKGROUND Pulmonary artery aneurysms are a rare condition, frequently associated with pulmonary hypertension. However, the evolution and treatment of this pathology is still not clear. CASE PRESENTATION The authors report a case of a 65-year old patient with pulmonary artery aneurysm associated with pulmonary arterial hypertension. Due to a positive vasoreactivity test, treatment with calciu...

Unilateral absence of a pulmonary artery (UAPA) is a rare pulmonary vascular anomaly that is usually associated with other cardiac anomalies. We report a 9-year-old female diagnosed with isolated unilateral absence of the left pulmonary artery and a right aortic arch but without other cardiac anomalies. The only symptoms the patient had were recurrent respiratory tract infections. The chest x-r...

Abstract Congenitally Corrected Transposition of Great Arteries is a unique condition in which atrio-ventricular discrepancy e ventricular-arteriosus are mutually balanced, so that there the normal oxygenation and distribution blood to tissues, but morphologically right ventricle tricuspid valve have deal with systemic pressures, developing severe ventricular disfunction regurgitation along yea...

BACKGROUND In spontaneously breathing cardiac patients, pulmonary artery pressure (PAP) can be accurately estimated from the transthoracic Doppler study of pulmonary artery and tricuspid regurgitation blood flows. In critically ill patients on mechanical ventilation for acute lung injury, the interposition of gas between the probe and the heart renders the transthoracic approach problematic. Th...

OBJECTIVES This study investigated the pharmacologic effect of endothelin receptor antagonists on cardiopulmonary hemodynamic variables in a beagle model of pulmonary hypertension. BACKGROUND We recently developed a beagle model of pulmonary hypertension that allows accurate determination of cardiopulmonary hemodynamic variables and is associated with elevated plasma endothelin-1 concentratio...