Echocardiographic studies have demonstrated that the characteristic anatomic defect in idiopathic hypertrophic subaortic stenosis (IHSS) is asymmetric septal hypertrophy (ASH). Although echocardiographic diagnosis of ASH is extremely sensitive, occasionally adequate echocardiograms cannot be obtained. Moreover, echocardiographic assessment of the extent of the underlying cardiomyopathic process...

This case report describes the distinctive echocardiographic pattern in a patient with a congenital right sinus of Valsalva aneurysm. The eChocardiogram demonstrated an abnormal structure extending from the aortic root into the left ventricular chamber adjacent to the interventricular septum. The structure showed diastolic motion away from the septum and systolic motion toward the septum. This ...

Depolarization of the atrioventricular junctional tissues and of the atrial septum was examined in the perfused dog heart before and during ventricular fibrillation by (1) recording the potentials from the junctional tissues in the regions of the interatrial and interventricular septum and examining the relationship of activity at these sites to atrial depolarization, (2) computing histograms a...

One hundred and one patients with sustained unimorphic ventricular tachycardia underwent programmed ventricular stimulation with one of two protocols. Fifty patients underwent programmed stimulation with protocol A, which consisted of burst overdrive pacing, single, double, and triple extrastimuli at the right ventricular apex, right ventricular outflow tract, or septum, and then at the left ve...

The records of 15 infants with pulmonary atresia and 19 infants with critical pulmonic stenosis and intact ventricular septum, all under 1 year of age, have been reviewed. Symptoms started earlier and were more severe in the group with pulmonary atresia. All patients showed arterial unsaturation, and many had congestive heart failure. The electrocardiogram was the most helpful tool in different...

Roger' in 1879 was the first to describe a congenital defect of the heart in which symptoms were absent, although definite, constant, and characteristic physical signs were present. An interesting feature of his description was that his observations were unsupported by an autopsy on the case that he described. However, so definite was the syndrome that Dupre", who verified a case at autopsy in ...

Asymmetric septal hypertrophy, or ASH, is a genetically determined myocardial disorder that is transmitted as an autosomal dominant trait. ASH is characterized by a disproportionately thickened ventricular septum that contains numerous hypertrophied, bizarrely-shaped and disorganized cardiac muscle cells. Disproportionate hypertrophy of the ventricular septum has also been observed in associati...

Increasingly sophisticated echocardiographic procedures are revealing previously unknown details of well known structures such as the interventricular septum.