OBJECTIVE We analyzed the electroclinical features, etiology, treatment, and outcome of 12 patients with West syndrome (WS) associated with focal hypsarrhythmia (FH). METHODS Between February 2005 and July 2013, 12 patients met the electroclinical diagnostic criteria of WS associated with FH. Hypsarrhythmia was considered to be focal when two or three brain lobes were involved. Patients with ...

Progressive facial hemiatrophy, also known as Parry-Romberg syndrome, is a progressive and self-limited deformation of the subcutaneous tissue volume on one side of the face that creates craniofacial asymmetry. We present the case of a patient with a five-year history of progressive right facial hemiatrophy, who underwent facial volumetric restoration using cell-assisted lipotransfer (CAL), whi...

A 46-year-old woman who presented with progressive facial hemiatrophy (PFH) following localized scleroderma is described. The patient had a markedly deformed and depressed plaque surrounded by erythema on the right cheek. She also showed linear scleroderma with hair loss on the occipital area and morphea lesions on the neck and shoulder. Histological findings of the facial and other atrophic le...

Progressive facial hemiatrophy or Parry-Romberg Syndrome is a rare disease characterized by atrophy in subcutaneous tissues on skin on one half of the face and some accompanied systematic findings. Generally, it develops before the age of 20. It is quite difficult to discriminate it from linear scleroderma localized in fronto-parietal area as they have similar clinical characteristics. In this ...

Sturge-Weber syndrome is a rare condition first described by Sturge in 1879 in a case report of an epileptic patient [1] . The association of intracranial calcifications was subsequently described by Weber in 1922, giving this condition its familiar eponym [2] . The classical findings include gyriform intracranial calcifications, congenital and usually unilateral capillary facial nevus, convuls...

A 50 year old male with obstructive sleep apnea developed de novo, daily, intense, continuous, left side pounding headache with superimposed stabbing pains, fluctuating in severity. Headache was associated with ptosis of the left eye, left hypoglossal palsy and eventual tongue hemiatrophy, in the absence of papilledema. His Brain and neck imaging procedures (MRI, MRA, MRV) and a left temporal a...