Fourty-three operations were performed on a total of 41 patients consisting of atrial septal defect, ventricular septal defect, ventricular septal defect with pulmonary stenosis, tetralogy of Fallot, aortic valve stenosis, pulmonary valve stenosis and coarctation of the aorta under hypothermia using intrathoracic rewarming. All patients but 2 cases with tetralogy Fallot have been completely cur...

Background Cardiac MRI is used to measure right ventricular end diastolic volume indexed to body surface area (RVEDVi) and ejection fraction (EF) in the setting of pulmonary insufficiency (PI). There is data describing optimum RVEDVi, in tetralogy of fallot (TOF) patients, to provide a competent pulmonary valve and maintain long term RV function. Pulmonary atresia with intact ventricular septum...

A 69-year-old woman with known hypertension and atrial septal defect (ASD) presented with dyspnea on exertion and generalized edema. A grade 3/6 systolic murmur was heard at the left sternal border. Electrocardiography showed complete right bundle branch block and a chest radiography showed progressive cardiomegaly and pulmonary edema. Two-dimensional transthoracic echocardiography (TTE) showed...

N oonan syndrome (MIM 163950), an autosomal dominant disorder with an estimated prevalence of 1/1000– 2500 at birth, is characterised by short stature, facial anomalies, pterygium colli, and congenital heart disease. 2 Although pulmonary valve stenosis with dysplastic leaflets, hypertrophic cardiomyopathy, and atrial septal defects (ASD) are the most common congenital heart defects in Noonan sy...

N oonan syndrome (MIM 163950), an autosomal dominant disorder with an estimated prevalence of 1/1000– 2500 at birth, is characterised by short stature, facial anomalies, pterygium colli, and congenital heart disease. 2 Although pulmonary valve stenosis with dysplastic leaflets, hypertrophic cardiomyopathy, and atrial septal defects (ASD) are the most common congenital heart defects in Noonan sy...

Pulmonary stenosis (PS) can be seen from the right ventricular outflow tract to the peripheral pulmonary arteries. Most frequently, the obstruction occurs at the level of the pulmonary valve; however, it occurs less frequently at the infindibular level within the trabecular component of the right ventricle or within the pulmonary arterial pathways. Lesions at any of these levels can occur as pa...

The electrocardiograms in 32 patients with mitral valve disease have been compared with the pulmonary resistances, the pulmonary artery pressures, and the size of the mitral valve orifice. In patients with pure stenosis if the electrocardiogram showed the pattern of right ventricular hyper-trophy the total pulmonary resistance was usually 1000 dynes seconds cm.-5 or greater. If mitral insuffici...

Isolated pulmonary valve endocarditis is an uncommon clinical entity and is usually associated with intravenous drug abuse. The majority of cases involve the tricuspid valve. Isolated pulmonary valve bacterial endocarditis complicating Triology of Fallot ( which constitutes pulmonary valve stenosis, right ventricular hypertrophy and atrial septal defect) is very rare. A rare complication of a r...

It has been suggested that the maximal amplitude of the pulmonary valve motion following atrial contraction (Amax) may be useful in the clinical evaluation of patients with valvular pulmonary stenosis. To evaluate the specificity and sensitivity of this measurement in children, we reviewed the echocardiograms of the pulmonary valve of 120 subjects: 57 normal individuals, 25 patients with secund...