After a difficult nasal intubation a premature infant leaked cerebrospinal fluid (CSF) from one nostril. After developing bacterial meningitis, the baby was referred for neurosurgical management of the CSF fistula. Transaxial computed tomograms demonstrated a nasal encephalocele, but coronal scans were needed to show the defect in the cribriform plate.

Our patient had an anterior encephalocele accompanied by teratoma. According to our extensive literature review, this association was very rarely reported so far[2,4]. Several hypotheses had been suggested to describe the pathogenesis of encephaloceles or teratomas but association of two entities cannot be simply explained by these models. Enrolment of tissue induction through different steps o...

Meckel-Gruber syndrome is a monogenic congenital disorder characterized by occipital encephalocele, polydactyly, and polycystic kidneys. This incompatible with life. We report case diagnosed on fetal ultrasound at gestational age of 22 SA 6 days, presenting the clinical triad syndrome. A medical termination pregnancy was indicated. From this rare case, through review literature, we will discuss...