Leading symptoms of anorectal malformation in the neonatal period are abdominal distention, non-passage of meconium and constipation. When present, vomiting is a late symptom. In a study in Calabar, Nigeria, patients were observed to present late, and teenage mothers in rural communities were mostly affected. Female neonates were affected more than males in a ratio of 1.5:1. Classification into...

BACKGROUND Although anorectal malformations (ARMs) are frequently encountered, rare variants difficult to classify have been reported. METHODS This study describes a patient with ARM and rectopenile fistula. The literature was reviewed systematically to assess the anatomical characteristics, clinical presentations and operations of this rare type of ARM. RESULTS Eight patients were reported...

OBJECTIVE We present a case of split notochord syndrome, an extremely rare form of spinal dysraphism. DESCRIPTION We treated a 2 month-old boy presenting with an extensive lumbosacral deformity, hydrocephalus and apparent enteric segments in the dorsal midline, accompanied by an enteric fistula and imperforated anus. The malformation was diagnosed as split notochord syndrome. The baby died as...

A 4-day-old male newborn, weighing 2.5 Kg, delivered vaginally at 38 weeks presented with malformed external genitalia and a reddish swelling over the lower part of the abdomen and the absent anal opening with a small perineal opening. Pregnancy was uneventful. Maternal serologies for HbsAg, HCV, HIV, Toxoplasma, and Rubella were planned but due to financial reason not done. Physical examinatio...

A 7-days-old male neonate with anorectal malformation (ARM) presented with abdominal distension and bleeding per rectum. He had an operation for ARM (Anoplasty) a day after birth and the patient had history of passing stool normally for two days. It was followed by blood mixed stool and abdominal distension. On examination, the patient had features of mild dehydration and sepsis. The abdomen wa...

Mayer Rokitansky Kuster Houser syndrome (MRKH syndrome) is characterized by Mullerian duct structures agenesis, vaginal atresia being the commonest variant. It can be associated with renal, skeletal, spine and other malformations. Patient with Mayer Rokitansky syndrome has a varied presentation from newborn period to adolescence. Thorough investigations are required for classification of the sy...

Objective: To determine the incidence and types of associated anomalies in children with anorectal